ENZYME REPLACEMENT THERAPY IN GAUCHERS-DISEASE - LARGE-SCALE PURIFICATION OF GLUCOCEREBROSIDASE SUITABLE FOR HUMAN ADMINISTRATION

被引：160

作者：

FURBISH, FS

BLAIR, HE

SHILOACH, J

PENTCHEV, PG

BRADY, RO

机构：

[1] NINCDS,DEV & METAB NEUROL BRANCH,BETHESDA,MD

[2] TUFTS UNIV,SCH MED,NEW ENGLAND ENZYME CTR,BOSTON,MA 02111

来源：

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA | 1977年 / 74卷 / 08期

关键词：

D O I：

10.1073/pnas.74.8.3560

中图分类号：

O [数理科学和化学]; P [天文学、地球科学]; Q [生物科学]; N [自然科学总论];

学科分类号：

07 ; 0710 ; 09 ;

摘要：

引用

页码：3560 / 3563

页数：4

共 19 条

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[2] ASSAY OF PROTEINS IN PRESENCE OF INTERFERING MATERIALS
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[3] METABOLISM OF GLUCOCEREBROSIDES .2. EVIDENCE OF AN ENZYMATIC DEFICIENCY IN GAUCHERS DISEASE
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[J]. BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1965, 18 (02) : 221 - &
[4] REPLACEMENT THERAPY FOR INHERITED ENZYME DEFICIENCY - USE OF PURIFIED GLUCOCEREBROSIDASE IN GAUCHERS-DISEASE
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[J]. NEW ENGLAND JOURNAL OF MEDICINE, 1974, 291 (19) : 989 - 993
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[6] SOLUBILIZATION OF GLUCOCEREBROSIDASE FROM HUMAN PLACENTA AND DEMONSTRATION OF A PHOSPHOLIPID REQUIREMENT FOR ITS CATALYTIC ACTIVITY
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[J]. BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1976, 71 (04) : 1048 - 1053
[7] ENZYME REPLACEMENT THERAPY IN GAUCHERS-DISEASE - RAPID, HIGH-YIELD METHOD FOR PURIFICATION OF GLUCOCEREBROSIDASE
DALE, GL
BEUTLER, E
[J]. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1976, 73 (12) : 4672 - 4674
[8] GLEW RH, 1973, J BIOL CHEM, V218, P3137
[9] EUKARYOTE RIBOSOMES POSSESS A BINDING-SITE FOR CONCANAVALIN-A
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[J]. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1977, 74 (03) : 818 - 821
[10] KANFER JN, 1966, J BIOL CHEM, V241, P1081

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