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HUMAN BETA-GLUCURONIDASE .1. RECOGNITION AND UPTAKE BY ANIMAL FIBROBLASTS SUGGESTS ANIMAL-MODELS FOR ENZYME REPLACEMENT STUDIES
被引:18
作者
:
FRANKEL, HA
论文数:
0
引用数:
0
h-index:
0
机构:
ST LOUIS CHILDRENS HOSP,DEPT PEDIAT,DIV MED GENET,ST LOUIS,MO 63110
FRANKEL, HA
GLASER, JH
论文数:
0
引用数:
0
h-index:
0
机构:
ST LOUIS CHILDRENS HOSP,DEPT PEDIAT,DIV MED GENET,ST LOUIS,MO 63110
GLASER, JH
SLY, WS
论文数:
0
引用数:
0
h-index:
0
机构:
ST LOUIS CHILDRENS HOSP,DEPT PEDIAT,DIV MED GENET,ST LOUIS,MO 63110
SLY, WS
机构
:
[1]
ST LOUIS CHILDRENS HOSP,DEPT PEDIAT,DIV MED GENET,ST LOUIS,MO 63110
[2]
WASHINGTON UNIV,SCH MED,EDWARD MALLICKRODT DEPT PEDIAT,ST LOUIS,MO 63110
来源
:
PEDIATRIC RESEARCH
|
1977年
/ 11卷
/ 07期
关键词
:
D O I
:
10.1203/00006450-197707000-00007
中图分类号
:
R72 [儿科学];
学科分类号
:
100202 ;
摘要
:
引用
收藏
页码:811 / 816
页数:6
相关论文
共 18 条
[1]
IN-VITRO CORRECTION OF DEFICIENT HUMAN FIBROBLASTS BY BETA-GLUCURONIDASE FROM DIFFERENT HUMAN SOURCES
BROT, FE
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT PEDIAT, ST LOUIS, MO 63110 USA
BROT, FE
GLASER, JH
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT PEDIAT, ST LOUIS, MO 63110 USA
GLASER, JH
ROOZEN, KJ
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT PEDIAT, ST LOUIS, MO 63110 USA
ROOZEN, KJ
SLY, WS
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT PEDIAT, ST LOUIS, MO 63110 USA
SLY, WS
[J].
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS,
1974,
57
(01)
: 1
-
8
[2]
TOWARD ENZYME THERAPY FOR LYSOSOMAL STORAGE DISEASES
DESNICK, RJ
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MINNESOTA, DEPT PEDIAT, MINNEAPOLIS, MN 55455 USA
DESNICK, RJ
THORPE, SR
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MINNESOTA, DEPT PEDIAT, MINNEAPOLIS, MN 55455 USA
THORPE, SR
FIDDLER, MB
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MINNESOTA, DEPT PEDIAT, MINNEAPOLIS, MN 55455 USA
FIDDLER, MB
[J].
PHYSIOLOGICAL REVIEWS,
1976,
56
(01)
: 57
-
99
[3]
FELINE GM1 GANGLIOSIDOSIS - BIOCHEMICAL AND ULTRASTRUCTURAL COMPARISONS WITH DISEASE IN MAN
FARRELL, DF
论文数:
0
引用数:
0
h-index:
0
机构:
JOHNS HOPKINS UNIV, SCH MED, DEPT NEUROL, BALTIMORE, MD 21218 USA
FARRELL, DF
BAKER, HJ
论文数:
0
引用数:
0
h-index:
0
机构:
JOHNS HOPKINS UNIV, SCH MED, DEPT NEUROL, BALTIMORE, MD 21218 USA
BAKER, HJ
HERNDON, RM
论文数:
0
引用数:
0
h-index:
0
机构:
JOHNS HOPKINS UNIV, SCH MED, DEPT NEUROL, BALTIMORE, MD 21218 USA
HERNDON, RM
LINDSEY, JR
论文数:
0
引用数:
0
h-index:
0
机构:
JOHNS HOPKINS UNIV, SCH MED, DEPT NEUROL, BALTIMORE, MD 21218 USA
LINDSEY, JR
MCKHANN, GM
论文数:
0
引用数:
0
h-index:
0
机构:
JOHNS HOPKINS UNIV, SCH MED, DEPT NEUROL, BALTIMORE, MD 21218 USA
MCKHANN, GM
[J].
JOURNAL OF NEUROPATHOLOGY AND EXPERIMENTAL NEUROLOGY,
1973,
32
(01)
: 1
-
18
[4]
FIDDLER MB, 1974, ENZYME THERAPY LYSOS, P182
[5]
FRANKEL HA, 1975, PEDIATR RES, V9, P313
[6]
GLASER JH, 1973, J LAB CLIN MED, V82, P969
[7]
GENETIC-HETEROGENEITY IN MULTIPLE LYSOSOMAL HYDROLASE DEFICIENCY
GLASER, JH
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT PEDIAT, ST LOUIS, MO 63130 USA
GLASER, JH
MCALISTER, WH
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT PEDIAT, ST LOUIS, MO 63130 USA
MCALISTER, WH
SLY, WS
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT PEDIAT, ST LOUIS, MO 63130 USA
SLY, WS
[J].
JOURNAL OF PEDIATRICS,
1974,
85
(02)
: 192
-
198
[8]
MULTIPLE ISOELECTRIC AND RECOGNITION FORMS OF HUMAN BETA-GLUCURONIDASE ACTIVITY
GLASER, JH
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV,SCH MED,DEPT PEDIAT,ST LOUIS,MO 63130
GLASER, JH
ROOZEN, KJ
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV,SCH MED,DEPT PEDIAT,ST LOUIS,MO 63130
ROOZEN, KJ
BROT, FE
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV,SCH MED,DEPT PEDIAT,ST LOUIS,MO 63130
BROT, FE
SLY, WS
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV,SCH MED,DEPT PEDIAT,ST LOUIS,MO 63130
SLY, WS
[J].
ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS,
1975,
166
(02)
: 536
-
542
[9]
BETA-GLUCURONIDASE DEFICIENCY MUCOPOLYSACCHARIDOSIS - STUDIES IN CULTURED FIBROBLASTS
HALL, CW
论文数:
0
引用数:
0
h-index:
0
机构:
NIAMDD,BETHESDA,MD 20014
NIAMDD,BETHESDA,MD 20014
HALL, CW
CANTZ, M
论文数:
0
引用数:
0
h-index:
0
机构:
NIAMDD,BETHESDA,MD 20014
NIAMDD,BETHESDA,MD 20014
CANTZ, M
NEUFELD, EF
论文数:
0
引用数:
0
h-index:
0
机构:
NIAMDD,BETHESDA,MD 20014
NIAMDD,BETHESDA,MD 20014
NEUFELD, EF
[J].
ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS,
1973,
155
(01)
: 32
-
38
[10]
HYPOTHESIS FOR I-CELL DISEASE - DEFECTIVE HYDROLASES THAT DO NOT ENTER LYSOSOMES
HICKMAN, S
论文数:
0
引用数:
0
h-index:
0
HICKMAN, S
NEUFELD, EF
论文数:
0
引用数:
0
h-index:
0
NEUFELD, EF
[J].
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS,
1972,
49
(04)
: 992
-
&
←
1
2
→
共 18 条
[1]
IN-VITRO CORRECTION OF DEFICIENT HUMAN FIBROBLASTS BY BETA-GLUCURONIDASE FROM DIFFERENT HUMAN SOURCES
BROT, FE
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT PEDIAT, ST LOUIS, MO 63110 USA
BROT, FE
GLASER, JH
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT PEDIAT, ST LOUIS, MO 63110 USA
GLASER, JH
ROOZEN, KJ
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT PEDIAT, ST LOUIS, MO 63110 USA
ROOZEN, KJ
SLY, WS
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT PEDIAT, ST LOUIS, MO 63110 USA
SLY, WS
[J].
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS,
1974,
57
(01)
: 1
-
8
[2]
TOWARD ENZYME THERAPY FOR LYSOSOMAL STORAGE DISEASES
DESNICK, RJ
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MINNESOTA, DEPT PEDIAT, MINNEAPOLIS, MN 55455 USA
DESNICK, RJ
THORPE, SR
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MINNESOTA, DEPT PEDIAT, MINNEAPOLIS, MN 55455 USA
THORPE, SR
FIDDLER, MB
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MINNESOTA, DEPT PEDIAT, MINNEAPOLIS, MN 55455 USA
FIDDLER, MB
[J].
PHYSIOLOGICAL REVIEWS,
1976,
56
(01)
: 57
-
99
[3]
FELINE GM1 GANGLIOSIDOSIS - BIOCHEMICAL AND ULTRASTRUCTURAL COMPARISONS WITH DISEASE IN MAN
FARRELL, DF
论文数:
0
引用数:
0
h-index:
0
机构:
JOHNS HOPKINS UNIV, SCH MED, DEPT NEUROL, BALTIMORE, MD 21218 USA
FARRELL, DF
BAKER, HJ
论文数:
0
引用数:
0
h-index:
0
机构:
JOHNS HOPKINS UNIV, SCH MED, DEPT NEUROL, BALTIMORE, MD 21218 USA
BAKER, HJ
HERNDON, RM
论文数:
0
引用数:
0
h-index:
0
机构:
JOHNS HOPKINS UNIV, SCH MED, DEPT NEUROL, BALTIMORE, MD 21218 USA
HERNDON, RM
LINDSEY, JR
论文数:
0
引用数:
0
h-index:
0
机构:
JOHNS HOPKINS UNIV, SCH MED, DEPT NEUROL, BALTIMORE, MD 21218 USA
LINDSEY, JR
MCKHANN, GM
论文数:
0
引用数:
0
h-index:
0
机构:
JOHNS HOPKINS UNIV, SCH MED, DEPT NEUROL, BALTIMORE, MD 21218 USA
MCKHANN, GM
[J].
JOURNAL OF NEUROPATHOLOGY AND EXPERIMENTAL NEUROLOGY,
1973,
32
(01)
: 1
-
18
[4]
FIDDLER MB, 1974, ENZYME THERAPY LYSOS, P182
[5]
FRANKEL HA, 1975, PEDIATR RES, V9, P313
[6]
GLASER JH, 1973, J LAB CLIN MED, V82, P969
[7]
GENETIC-HETEROGENEITY IN MULTIPLE LYSOSOMAL HYDROLASE DEFICIENCY
GLASER, JH
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT PEDIAT, ST LOUIS, MO 63130 USA
GLASER, JH
MCALISTER, WH
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT PEDIAT, ST LOUIS, MO 63130 USA
MCALISTER, WH
SLY, WS
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT PEDIAT, ST LOUIS, MO 63130 USA
SLY, WS
[J].
JOURNAL OF PEDIATRICS,
1974,
85
(02)
: 192
-
198
[8]
MULTIPLE ISOELECTRIC AND RECOGNITION FORMS OF HUMAN BETA-GLUCURONIDASE ACTIVITY
GLASER, JH
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV,SCH MED,DEPT PEDIAT,ST LOUIS,MO 63130
GLASER, JH
ROOZEN, KJ
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV,SCH MED,DEPT PEDIAT,ST LOUIS,MO 63130
ROOZEN, KJ
BROT, FE
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV,SCH MED,DEPT PEDIAT,ST LOUIS,MO 63130
BROT, FE
SLY, WS
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV,SCH MED,DEPT PEDIAT,ST LOUIS,MO 63130
SLY, WS
[J].
ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS,
1975,
166
(02)
: 536
-
542
[9]
BETA-GLUCURONIDASE DEFICIENCY MUCOPOLYSACCHARIDOSIS - STUDIES IN CULTURED FIBROBLASTS
HALL, CW
论文数:
0
引用数:
0
h-index:
0
机构:
NIAMDD,BETHESDA,MD 20014
NIAMDD,BETHESDA,MD 20014
HALL, CW
CANTZ, M
论文数:
0
引用数:
0
h-index:
0
机构:
NIAMDD,BETHESDA,MD 20014
NIAMDD,BETHESDA,MD 20014
CANTZ, M
NEUFELD, EF
论文数:
0
引用数:
0
h-index:
0
机构:
NIAMDD,BETHESDA,MD 20014
NIAMDD,BETHESDA,MD 20014
NEUFELD, EF
[J].
ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS,
1973,
155
(01)
: 32
-
38
[10]
HYPOTHESIS FOR I-CELL DISEASE - DEFECTIVE HYDROLASES THAT DO NOT ENTER LYSOSOMES
HICKMAN, S
论文数:
0
引用数:
0
h-index:
0
HICKMAN, S
NEUFELD, EF
论文数:
0
引用数:
0
h-index:
0
NEUFELD, EF
[J].
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS,
1972,
49
(04)
: 992
-
&
←
1
2
→