COMPLETE PRIMARY STRUCTURE OF THE TRANSACYLASE (E2B) SUBUNIT OF THE HUMAN BRANCHED-CHAIN ALPHA-KETO ACID DEHYDROGENASE COMPLEX

被引:30
作者
NOBUKUNI, Y [1 ]
MITSUBUCHI, H [1 ]
ENDO, F [1 ]
MATSUDA, I [1 ]
机构
[1] KUMAMOTO UNIV,SCH MED,DEPT PEDIAT,KUMAMOTO 860,JAPAN
关键词
D O I
10.1016/0006-291X(89)91347-8
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:1035 / 1041
页数:7
相关论文
共 27 条
[1]  
CHUANG DT, 1984, J BIOL CHEM, V259, P9277
[2]  
CHUANG DT, 1985, J BIOL CHEM, V260, P3779
[3]   RESOLUTION AND RECONSTITUTION OF BOVINE KIDNEY BRANCHED-CHAIN 2-OXO ACID DEHYDROGENASE COMPLEX [J].
COOK, KG ;
BRADFORD, A ;
YEAMAN, SJ .
BIOCHEMICAL JOURNAL, 1985, 225 (03) :731-735
[4]   PURIFICATION AND PROPERTIES OF BRANCHED-CHAIN ALPHA-KETO ACID DEHYDROGENASE PHOSPHATASE FROM BOVINE KIDNEY [J].
DAMUNI, Z ;
MERRYFIELD, ML ;
HUMPHREYS, JS ;
REED, LJ .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1984, 81 (14) :4335-4338
[5]  
DANNER DJ, 1979, J BIOL CHEM, V254, P5522
[6]   ABSENCE OF BRANCHED-CHAIN ACYL-TRANSFERASE AS A CAUSE OF MAPLE SYRUP URINE DISEASE [J].
DANNER, DJ ;
ARMSTRONG, N ;
HEFFELFINGER, SC ;
SEWELL, ET ;
PRIEST, JH ;
ELSAS, LJ .
JOURNAL OF CLINICAL INVESTIGATION, 1985, 75 (03) :858-860
[7]   DEPHOSPHORYLATION AND REACTIVATION OF PHOSPHORYLATED PURIFIED OX-KIDNEY BRANCHED-CHAIN DEHYDROGENASE COMPLEX BY CO-PURIFIED PHOSPHATASE [J].
FATANIA, HR ;
PATSTON, PA ;
RANDLE, PJ .
FEBS LETTERS, 1983, 158 (02) :234-238
[8]  
GRIFFIN TA, 1988, J BIOL CHEM, V263, P14008
[9]   DIDEOXY SEQUENCING METHOD USING DENATURED PLASMID TEMPLATES [J].
HATTORI, M ;
SAKAKI, Y .
ANALYTICAL BIOCHEMISTRY, 1986, 152 (02) :232-238
[10]   IDENTIFICATION OF SPECIFIC SUBUNITS OF HIGHLY PURIFIED BOVINE LIVER BRANCHED-CHAIN KETOACID DEHYDROGENASE [J].
HEFFELFINGER, SC ;
SEWELL, ET ;
DANNER, DJ .
BIOCHEMISTRY, 1983, 22 (24) :5519-5522