ENZYME REPLACEMENT TREATMENT FOR TAY-SACHS DISEASE BRAIN-CELLS IN CULTURE UTILIZING CONCANAVALIN A-MEDIATED HEXOSAMINIDASE-A UPTAKE - BIOCHEMICAL AND MORPHOLOGICAL EVIDENCE OF GM2 MOBILIZATION

被引：18

作者：

BROOKS, SE ^{[1
]}

HOFFMAN, LM ^{[1
]}

ADACHI, M ^{[1
]}

AMSTERDAM, D ^{[1
]}

SCHNECK, L ^{[1
]}

机构：

[1] SUNY DOWNSTATE MED CTR,BROOKLYN,NY 11203

来源：

ACTA NEUROPATHOLOGICA | 1980年 / 50卷 / 01期

关键词：

D O I：

10.1007/BF00688529

中图分类号：

R74 [神经病学与精神病学];

学科分类号：

摘要：

引用

页码：9 / 17

页数：9

共 31 条

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[2]

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VOLK, BW .

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[4]

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[5] EFFECT OF LECTINS ON ENDOCYTOSIS AND SECRETION OF LYSOSOMAL ENZYMES BY CULTURED FIBROBLASTS [J].

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ULLRICH, K ;

VONFIGURA, K .

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[6]

BROOKS SE, 1979, J CELL SCI, V38, P211

[7] IN-VITRO CORRECTION OF DEFICIENT HUMAN FIBROBLASTS BY BETA-GLUCURONIDASE FROM DIFFERENT HUMAN SOURCES [J].

BROT, FE ;

GLASER, JH ;

ROOZEN, KJ ;

SLY, WS .

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[8] INTRODUCTION OF PURIFIED HEXOSAMINIDASE-A INTO TAY-SACHS LEUKOCYTES BY MEANS OF IMMUNOGLOBULIN-COATED LIPOSOMES [J].

COHEN, CM ;

WEISSMANN, G ;

HOFFSTEIN, S ;

AWASTHI, YC ;

SRIVASTAVA, SK .

BIOCHEMISTRY, 1976, 15 (02) :452-460

[9]

DAWSON G, 1972, J BIOL CHEM, V247, P5951

[10] CONCANAVALIN A MEDIATED UPTAKE OF ENZYMES BY FIBROBLASTS [J].

GONZALEZNORIEGA, A ;

SLY, WS .

BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1978, 85 (01) :174-182

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