INCREASED EXCRETION OF A GLUCOSE-CONTAINING TETRASACCHARIDE IN URINE OF A PATIENT WITH GLYCOGEN-STORAGE DISEASE TYPE-II (POMPES DISEASE)

被引:41
作者
HALLGREN, P
HANSSON, G
HENRIKSSON, KG
HAGER, A
LUNDBLAD, A
SVENSSON, S
机构
[1] UNIV UPPSALA, INST MED CHEM, UPPSALA, SWEDEN
[2] UNIV STOCKHOLM, DEPT ORG CHEM, STOCKHOLM, SWEDEN
[3] UNIV HOSP LINKOPING, DEPT PEDIAT, LINKOPING, SWEDEN
[4] UNIV HOSP LINKOPING, DEPT CLIN NEUROPHYSIOL, LINKOPING, SWEDEN
关键词
D O I
10.1111/j.1365-2362.1974.tb00416.x
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:429 / 433
页数:5
相关论文
共 24 条
[1]  
BERGGARD I, 1962, ARK KEMI, V18, P291
[2]  
DISCHE Z, 1948, J BIOL CHEM, V175, P595
[4]  
HUTTUNEN JK, 1966, ANN MED EXP FENN S, V12, P44
[5]  
JANSON JC, 1972, THESIS U UPPSALA
[6]  
KUNKEL HG, 1954, METHOD BIOCHEM ANAL, V1, P141
[7]   ISOLATION AND CHARACTERIZATION OF "3-0-ALPHA-D-XYLOPYRANOSYL-D-GLUCOSE AND "2-0-ALPHA-L-FUCOPYRANOSYL-D-GLUCOSE FROM NORMAL HUMAN URINE [J].
LUNDBLAD, A ;
SVENSSON, S .
BIOCHEMISTRY, 1973, 12 (02) :306-308
[8]   ISOLATION AND CHARACTERIZATION OF A URINARY OLIGOSACCHARIDE CHARACTERISTIC OF BLOOD GROUP O(H)-SECRETORS [J].
LUNDBLAD, A .
BIOCHIMICA ET BIOPHYSICA ACTA, 1968, 165 (02) :202-&
[9]   STRUCTURES AND SEROLOGICAL ACTIVITIES OF THREE OLIGOSACCHARIDES ISOLATED FROM URINES OF NONSTARVED SECRETORS AND FROM SECRETORS ON LACTOSE DIET [J].
LUNDBLAD, A ;
HALLGREN, P ;
RUDMARK, A ;
SVENSSON, S .
BIOCHEMISTRY, 1973, 12 (17) :3341-3345