INTESTINAL ENTEROKINASE DEFICIENCY

被引:7
作者
FOLLETT, GF
MACDONALD, TH
机构
[1] DEPT BIOCHEM, FALKIRK, SCOTLAND
[2] DEPT CHILD HLTH, FALKIRK, SCOTLAND
[3] DIST ROY INFIRM, FALKIRK FK1 5QE, SCOTLAND
来源
ACTA PAEDIATRICA SCANDINAVICA | 1976年 / 65卷 / 05期
关键词
D O I
10.1111/j.1651-2227.1976.tb04948.x
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Deficiency of intestinal enterokinase results in failure to thrive, diarrhea, anemia, hypoproteinemia and edema. A case arising in the neonatal period is described, in which several of the characteristic features were lacking. Difficulties encountered in the diagnosis and methods of assay are discussed.
引用
收藏
页码:653 / 655
页数:3
相关论文
共 10 条
[1]   PREPARATION AND PROPERTIES OF 2 NEW CHROMOGENIC SUBSTRATES OF TRYPSIN [J].
ERLANGER, BF ;
COHEN, W ;
KOKOWSKY, N .
ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS, 1961, 95 (02) :271-&
[2]  
FOLK JE, 1960, J BIOL CHEM, V235, P60
[3]  
HADORN B, 1969, LANCET, V1, P812
[4]  
HAWORTH JC, 1975, ARCH DIS CHILD, V50, P277
[5]   MALABSORPTION AND GROWTH FAILURE DUE TO INTESTINAL ENTEROKINASE DEFICIENCY [J].
HAWORTH, JC ;
GOURLEY, B ;
HADORN, B ;
SUMIDA, C .
JOURNAL OF PEDIATRICS, 1971, 78 (03) :481-+
[6]   A MODIFIED SPECTROPHOTOMETRIC DETERMINATION OF CHYMOTRYPSIN, TRYPSIN, AND THROMBIN [J].
HUMMEL, BCW .
CANADIAN JOURNAL OF BIOCHEMISTRY AND PHYSIOLOGY, 1959, 37 (12) :1393-1399
[7]  
POLONOVSKI C, 1970, ACTA PAEDIATR SCAND, V59, P458
[8]   DETERMINATION OF AMYLASE ACTIVITY IN BIOLOGICAL FLUIDS [J].
STREET, HV ;
CLOSE, JR .
CLINICA CHIMICA ACTA, 1956, 1 (03) :256-268
[9]   INTESTINAL ENTEROKINASE DEFICIENCY - A NEWLY-RECOGNIZED DISORDER OF PROTEIN DIGESTION [J].
TARLOW, MJ ;
HADORN, B ;
ARTHURTON, MW ;
LLOYD, JK .
ARCHIVES OF DISEASE IN CHILDHOOD, 1970, 45 (243) :651-+
[10]  
VARLEY H, 1967, PRACTICAL CLINICAL B, P408