IgA血管炎的免疫机制和治疗现状及展望

被引:5
作者
杨思睿
刘德滢
王晶华
刘金香
刘聪聪
机构
[1] 长春,吉林大学第一医院儿童风湿免疫过敏科
关键词
IgA血管炎; 发病机制; 治疗; 糖皮质激素;
D O I
暂无
中图分类号
R725.5 [小儿血液及淋巴系疾病]; R725.9 [小儿全身性疾病];
学科分类号
100201 [内科学];
摘要
IgA血管炎(IgAV)是以小血管为主要病变的系统性血管炎, 以非血小板减少性紫癜、关节痛、腹痛及肾炎为主要临床表现, 病因及发病机制尚待进一步深入了解。多数患儿病程具有自限性, 重症或迁延病例的治疗方案尚待进一步完善, 对关键药物的使用尚缺乏可靠的循证依据。期待更多严谨的临床试验, 以建立更加科学完整的疾病评价和预判体系, 以确立更科学合理的个体化治疗方案。
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