家族性肝内胆汁淤积症

被引：6

作者：

晏晓敏

黄志华

机构：

[1] 华中科技大学同济医学院附属同济医院儿科

来源：

临床儿科杂志 | 2011年 / 29卷 / 03期

关键词：

D O I：

暂无

中图分类号：

R714.2 [病理妊娠（异常妊娠）];

学科分类号：

100211 [妇产科学];

摘要：

<正>近年来,随着分子遗传学研究的进展,已证实家族性肝内胆汁淤积症(familial intrahepatic cholestasis,FIC)与一些特定的基因发生突变有关,由于基因突变致肝细胞或毛细胆管上皮细胞的胆汁分泌转运体缺失,导致胆汁分泌或

引用

页码：293 / 296

页数：4

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