噬血细胞综合征的研究进展

被引:23
作者
李强
机构
[1] 四川大学华西第二医院儿科成都
关键词
噬血细胞综合征,家族性; 噬血细胞综合征,继发性; EB病毒;
D O I
暂无
中图分类号
R725.5 [小儿血液及淋巴系疾病];
学科分类号
摘要
<正> 噬血细胞综合征(HPS)又称噬血细胞性淋巴组织增生症(HLH),是一种反应性单核吞噬系统疾病,常见于小儿,临床酷似恶性组织细胞增生症,易误诊。本病分为原发性和继发性两种,两者临床经过及预后均不同。本文就近年来此病的研究进展综述如下。
引用
收藏
页码:61 / 63
页数:3
相关论文
共 9 条
[1]  
Epstein-Barr virus-associated hemophagocytic syndrome. Kikuta H. Leukemia and Lymphoma . 1995
[2]  
Treatment of hemophagocytic lymphohistiocytosis with HLH-94 immunochemotherapy and bone marrow transplantation. Henter JI,Samuelsson-Horne A,Arico M,et al. Blood . 2002
[3]  
Epstein-Barr virus(EBV)infects T lymphocytes in childhood EBV-associated hemophagocytic syndrome in Taiwan. Su IJ,Chen RL,Lin DT,et al. American Journal of Pathology . 1994
[4]  
Perforin gene defects in familial hemophagocytic lymphohistiocytosis. Stepp SE,Dufourcq-Lagelouse R,Le Doist F,et al. Science . 1999
[5]  
Fulminant childhood hemophagocytic syndrome mimicking histiocytic medullary reticulosis: an atypical form of Epstein-Barr virus infection. Chen RL,Su IJ,Lin KH,et al. American Journal of Clinical Pathology . 1991
[6]  
Familial hemophagocytic lymphohistiocytosis: diagnosis, treatment and pathophsiological mechanisms. Henter JI,Samuelsson A,Ericson K,et al. Lakartidningen . 2000
[7]  
Hemophagocytic lymphohistoicytosis in infancy and childhood. Imashuku S,Hibi S,Todo S,et al. The Journal of Pediatrics . 1997
[8]  
Biology and treatment of familial hemophagocytic lymphohistiocytosis: importance of perforin in lymphocyte-mediated cytotoxicity and triggering of apoptosis. Henter JI. Medical and Pediatric Oncology . 2002
[9]  
Requirement for etoposide in the treatment of Epstein-Barr virus-associated hemophagocytic lymphohistiocytosis. Imashuku S,Kuriyama K,Teramura T,et al. Journal of Clinical Oncology . 2001