Steroid-responsive pulmonary hypertension in a patient with Langerhans' cell granulomatosis (histiocytosis X)

被引：23

作者：

Benyounes, B ^{[1
]}

Crestani, B ^{[1
]}

Couvelard, A ^{[1
]}

Vissuzaine, C ^{[1
]}

Aubier, M ^{[1
]}

机构：

[1] HOP BICHAT,DEPT PATHOL,PARIS,FRANCE

来源：

CHEST | 1996年 / 110卷 / 01期

关键词：

Langerhans' cell granulomatosis; pulmonary hypertension; steroids;

D O I：

10.1378/chest.110.1.284

中图分类号：

R4 [临床医学];

学科分类号：

1002 ; 100602 ;

摘要：

We report the case of a man with biopsy-proved pulmonary Langerhans' cells granulomatosis (histiocytosis X) and pulmonary precapillary hypertension. Pulmonary vascular resistances and mean pulmonary artery pressure decreased with corticosteroid therapy and dyspnea improved.

引用

页码：284 / 286

页数：3

共 6 条

[1] EOSINOPHILIC GRANULOMA OF LUNG - CLINICAL ASPECTS OF PRIMARY PULMONARY HISTIOCYTOSIS IN THE ADULT [J].