Long-QT Syndrome From Genetics to Management

被引：449

作者：

Schwartz, Peter J. ^{[1
,2
,3
,4
,5
]}

Crotti, Lia ^{[2
,6
]}

Insolia, Roberto ^{[2
]}

机构：

[1] Univ Pavia, Fdn IRCCS Policlin S Matteo, Dept Mol Med, I-27100 Pavia, Italy

[2] Fdn IRCCS Policlin S Matteo, Dept Cardiol, I-27100 Pavia, Italy

[3] Univ Cape Town, Dept Med, Hatter Inst Cardiovasc Res Africa, Cardiovasc Genet Lab, ZA-7925 Cape Town, South Africa

[4] Univ Stellenbosch, Dept Med, ZA-7600 Stellenbosch, South Africa

[5] King Saud Univ, Coll Med, Dept Family & Community Med, Chair Sudden Death, Riyadh 11461, Saudi Arabia

[6] Helmholtz Zentrum Munchen, Inst Human Genet, Neuherberg, Germany

来源：

CIRCULATION-ARRHYTHMIA AND ELECTROPHYSIOLOGY | 2012年 / 5卷 / 04期

基金：

美国国家卫生研究院;

关键词：

arrhythmia (heart rhythm disorders); beta-blockers; genetics; long-QT syndrome; sudden death; CARDIAC SYMPATHETIC DENERVATION; BETA-BLOCKER THERAPY; COMPOUND MUTATIONS; SCN5A MUTATIONS; MOLECULAR-BASIS; HEART-RATE; T-WAVE; RISK; ARRHYTHMIA; PHENOTYPE;

D O I：

10.1161/CIRCEP.111.962019

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

引用

页码：868 / 877

页数：10

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