Recurrence of desmoid tumor in a multivisceral transplant patient with Gardner's syndrome

Background Desmoid tumors are locally invasive fibromatous tumors, which, in patients with Gardner's syndrome, usually occur in the abdominal wall or intra-abdominally, After excision, they tend to recur, often leading to multiple bowel resections, Methods. This is a report of the clinical course of a patient with Gardner's syndrome and desmoid tumor who had multiple enterectomies and gradually developed short-gut syndrome. He required prolonged parenteral nutrition, which damaged the liver. The patient underwent a multivisceral transplantation as a life-saving procedure. Results. After the transplant, the desmoid tumor recurred in the thoracic wall twice and was successfully resected, It also recurred in the abdominal cavity, compressing the intestinal loops; the tumor was excised uneventfully, leaving the graft intact, The recurrent tumors were all of recipient origin, Conclusions. Intestinal and multivisceral transplantation could be considered in patients with short-gut syndrome caused by recurrent desmoid tumor. In the case of posttransplant tumor recurrence, resection is the only option recommended.