Thrombocytosis with sideroblastic erythropoiesis: A mixed myeloproliferative myelodysplastic syndrome

被引:23
作者
Gupta, R [1 ]
Abdalla, SH [1 ]
Bain, BJ [1 ]
机构
[1] Univ London Imperial Coll Sci Technol & Med, Dept Haematol, St Marys Hosp, Sch Med, London W2 1NY, England
关键词
myelodysplastic syndromes; myeloproliferative disorders; sideroblastic erythropoiesis; thrombocytosis;
D O I
10.3109/10428199909058492
中图分类号
R73 [肿瘤学];
学科分类号
100214 ;
摘要
Some patients with haematological neoplasms have features which overlap between a myelodysplastic syndrome and a myeloproliferative disorder. Two such patients are reported, both having sideroblastic erythropoiesis and thrombocytosis and one sequentially developing features of atypical chronic myeloid leukaemia, idiopathic myelofibrosis and acute megakaryoblastic leukaemia. The prevalence of thrombocytosis among cases of refractory anaemia with ring sideroblasts may be as high as 15-20% and has implications for choice of therapy.
引用
收藏
页码:615 / +
页数:6
相关论文
共 10 条
[1]  
CAZZOLA M, 1988, BLOOD, V71, P305
[2]  
CHENG DS, 1979, CANCER, V44, P724, DOI 10.1002/1097-0142(197908)44:2<724::AID-CNCR2820440245>3.0.CO
[3]  
2-W
[4]  
DEWALD GW, 1985, BLOOD, V66, P189
[5]   HETEROGENEITY OF ACQUIRED IDIOPATHIC SIDEROBLASTIC ANEMIA (AISA) [J].
GARAND, R ;
GARDAIS, J ;
BIZET, M ;
BREMOND, JL ;
ACCARD, F ;
CALLAT, MP ;
DEBOUCHONY, ET ;
GOASGUEN, JE .
LEUKEMIA RESEARCH, 1992, 16 (05) :463-468
[6]   PROGNOSTIC FACTORS OF MYELODYSPLASTIC SYNDROMES - A SIMPLIFIED 3-D SCORING SYSTEM [J].
GOASGUEN, JE ;
GARAND, R ;
BIZET, M ;
BREMOND, JL ;
GARDAIS, J ;
CALLAT, MP ;
ACCARD, F ;
CHAPERON, J .
LEUKEMIA RESEARCH, 1990, 14 (03) :255-262
[7]   HEMATOLOGICAL FEATURES OF PRIMARY MYELODYSPLASTIC SYNDROMES (PMDS) AT INITIAL PRESENTATION - A STUDY OF 118 CASES [J].
JUNEJA, SK ;
IMBERT, M ;
JOUAULT, H ;
SCOAZEC, JY ;
SIGAUX, F ;
SULTAN, C .
JOURNAL OF CLINICAL PATHOLOGY, 1983, 36 (10) :1129-1135
[8]   IDIOPATHIC REFRACTORY SIDEROBLASTIC ANEMIA - CLINICAL AND LABORATORY INVESTIGATION OF 17 PATIENTS AND REVIEW OF LITERATURE [J].
KUSHNER, JP ;
LEE, GR ;
WINTROBE, MM ;
CARTWRIGHT, GE .
MEDICINE, 1971, 50 (03) :139-+
[9]   Mixed myelodysplastic and myeloproliferative syndromes [J].
Neuwirtova, R ;
Mocikova, K ;
Musilova, J ;
Jelinek, J ;
Havlicek, F ;
Michalova, K ;
Adamkov, M .
LEUKEMIA RESEARCH, 1996, 20 (09) :717-726
[10]  
STREETER RR, 1977, BLOOD, V50, P427