Anaesthetic management of children with Joubert syndrome

被引：22

作者：

Habre, W ^{[1
]}

Sims, C ^{[1
]}

DSouza, M ^{[1
]}

机构：

[1] PRINCESS MARGARET HOSP CHILDREN,DEPT ANAESTHESIA,PERTH,WA 6001,AUSTRALIA

来源：

PAEDIATRIC ANAESTHESIA | 1997年 / 7卷 / 03期

关键词：

anaesthesia; neurological disorders; complications; apnoea; Joubert syndrome;

D O I：

10.1046/j.1460-9592.1997.d01-65.x

中图分类号：

R614 [麻醉学];

学科分类号：

100217 ;

摘要：

We report the anaesthetic management of two children with Joubert syndrome. Children with this syndrome have abnormalities of respiratory control due to changes in the brainstem and cerebellum. They are extremely sensitive to the respiratory depressant effects of anaesthetic agents, including nitrous oxide. Anaesthesia using inhalational induction, controlled ventilation, avoidance of opioids, and close postoperative monitoring is recommended.

引用

页码：251 / 253

页数：3

共 13 条

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