Persistent facial myokymia associated with K+ channel antibodies

被引:16
作者
Gutmann, L [1 ]
Tellers, JG
Vernino, S
机构
[1] W Virginia Univ, Dept Neurol, Robert C Byrd Hlth Sci Ctr, Morgantown, WV 26506 USA
[2] Mayo Clin, Dept Neurol, Rochester, MN USA
关键词
D O I
10.1212/WNL.57.9.1707
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
A 58-year-old woman developed bilateral facial myokymia in 1978, persisting for the next 23 years and associated with high titers of voltage-gated K+ channel (VGKC) antibodies. Brain imaging failed to show a pontine lesion. The clinical facial myokymia and electromyographic doublets and multiplets (43 to 250 Hz) were milder and more restricted than those seen in generalized neuromyotonic disorders with VGKC antibodies. This case and another reported recently represent a focal VGKC antibody syndrome.
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收藏
页码:1707 / 1708
页数:2
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