Megacystis - Microcolon - Intestinal hypoperistalsis syndrome

被引：5

作者：

Goldberg, M ^{[1
]}

Pruchniewski, D ^{[1
]}

Beale, PG ^{[1
]}

DaFonseca, JMB ^{[1
]}

Davies, MRQ ^{[1
]}

机构：

[1] UNIV WITWATERSRAND,SCH MED,DIV PAEDIAT SURG,JOHANNESBURG,SOUTH AFRICA

来源：

PEDIATRIC SURGERY INTERNATIONAL | 1996年 / 11卷 / 04期

关键词：

megacystis; microcolon; intestinal hypoperistalsis syndrome; family history; female cases;

D O I：

10.1007/BF00178429

中图分类号：

R72 [儿科学];

学科分类号：

100202 [儿科学];

摘要：

Two non-related female neonates with the megacystis-microcolon-intestinal hypoperistalsis syndrome are described. One presented with a family history of a similar condition. In one child no intestinal peristalsis was observed, while in the other decreased peristalsis with occasional rectal evacuation occurred. Both had fatal outcomes. These two cases demonstrate the wide variation in the clinical course of this rare and fatal syndrome.

引用

页码：246 / 247

页数：2

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