Serial MR imaging studies in enlarged endolymphatic duct and sac syndrome

被引:30
作者
Naganawa, Shinji [1 ]
Koshikawa, Tokiko [1 ]
Fukatsu, Hiroshi [1 ]
Ishigaki, Takeo [1 ]
Nakashima, Tsutomu [2 ]
机构
[1] Nagoya Univ, Dept Radiol, Sch Med, Shouwa Ku, Nagoya, Aichi 4668550, Japan
[2] Nagoya Univ, Dept Otolaryngol, Sch Med, Shouwa Ku, Nagoya, Aichi 4668550, Japan
关键词
Ear; Magnetic resonance; Abnormalities; Enlarged endolymphatic duct and sac syndrome;
D O I
10.1007/s00330-002-1525-9
中图分类号
R8 [特种医学]; R445 [影像诊断学];
学科分类号
1002 [临床医学]; 100207 [影像医学与核医学]; 1009 [特种医学];
摘要
Large vestibular aqueduct syndrome (LVAS) is a congenital disorder characterized by progressive or fluctuating sensorineural hearing loss of unknown etiology. Serial MR examinations were performed before and after the development of hearing loss in two patients with LVAS. The signal and volume of the enlarged endolymphatic sac (EES) vary even in ears with stable hearing. In ears with fluctuating hearing, changes in EES signals were observed in only one of two patients. The finding that the EES volume and signal intensity vary dynamically independently of hearing is important for future research into the pathophysiology of hearing loss in this syndrome.
引用
收藏
页码:S114 / S117
页数:4
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