Familial focal segmental glomerulosclerosis: Nine cases in four families and review of the literature

被引:22
作者
Faubert, PF [1 ]
Porush, JG [1 ]
机构
[1] BROOKDALE UNIV HOSP & MED CTR,DIV NEPHROL & HYPERTENS,DEPT MED,BROOKLYN,NY 11212
关键词
focal segmental glomerulosclerosis; idiopathic; familial;
D O I
10.1016/S0272-6386(97)90062-7
中图分类号
R5 [内科学]; R69 [泌尿科学(泌尿生殖系疾病)];
学科分类号
1002 ; 100201 ;
摘要
Idiopathic focal segmental glomerulosclerosis (FSGS) is a common cause of glomerular disease. Although previous case reports suggesting a familial form of the disease exist in the literature, its significance has not been emphasized. We report on our experience with nine cases in four families, as well as a review of the literature, and provide evidence that a familial form of FSGS might represent a distinct genotypic and phenotypic subset of idiopathic FSGS. (C) 1997 by the National Kidney Foundation, Inc.
引用
收藏
页码:265 / 270
页数:6
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