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Transmitochondrial mice carrying resistance to chloramphenicol on mitochondrial DNA: Developing the first mouse model of mitochondrial DNA disease
被引:51
作者
:
Marchington, DR
论文数:
0
引用数:
0
h-index:
0
机构:
John Radcliffe Hosp, Dept Paediat, Oxford OX3 9DU, England
Marchington, DR
Barlow, D
论文数:
0
引用数:
0
h-index:
0
机构:
John Radcliffe Hosp, Dept Paediat, Oxford OX3 9DU, England
Barlow, D
Poulton, J
论文数:
0
引用数:
0
h-index:
0
机构:
John Radcliffe Hosp, Dept Paediat, Oxford OX3 9DU, England
Poulton, J
机构
:
[1]
John Radcliffe Hosp, Dept Paediat, Oxford OX3 9DU, England
[2]
Univ Oxford, Nuffield Dept Obstet & Gynaecol, Oxford, England
来源
:
NATURE MEDICINE
|
1999年
/ 5卷
/ 08期
基金
:
英国惠康基金;
关键词
:
D O I
:
10.1038/11403
中图分类号
:
Q5 [生物化学];
Q7 [分子生物学];
学科分类号
:
071010 ;
081704 ;
摘要
:
引用
收藏
页码:957 / 960
页数:4
相关论文
共 17 条
[1]
EVIDENCE FROM MTDNA SEQUENCES THAT COMMON LABORATORY STRAINS OF INBRED MICE ARE DESCENDED FROM A SINGLE FEMALE
[J].
FERRIS, SD
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF BERKELEY,DEPT BIOCHEM,BERKELEY,CA 94720
FERRIS, SD
;
SAGE, RD
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF BERKELEY,DEPT BIOCHEM,BERKELEY,CA 94720
SAGE, RD
;
WILSON, AC
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF BERKELEY,DEPT BIOCHEM,BERKELEY,CA 94720
WILSON, AC
.
NATURE,
1982,
295
(5845)
:163
-165
[2]
MITOCHONDRIAL RIBOSOMAL-RNA GENE MUTATION IN A PATIENT WITH SPORADIC AMINOGLYCOSIDE OTOTOXICITY
[J].
FISCHELGHODSIAN, N
论文数:
0
引用数:
0
h-index:
0
FISCHELGHODSIAN, N
;
PREZANT, TR
论文数:
0
引用数:
0
h-index:
0
PREZANT, TR
;
BU, XD
论文数:
0
引用数:
0
h-index:
0
BU, XD
;
OZTAS, S
论文数:
0
引用数:
0
h-index:
0
OZTAS, S
.
AMERICAN JOURNAL OF OTOLARYNGOLOGY,
1993,
14
(06)
:399
-403
[3]
A mouse model for mitochondrial myopathy and cardiomyopathy resulting from a deficiency in the heart/muscle isoform of the adenine nucleotide translocator
[J].
Graham, BH
论文数:
0
引用数:
0
h-index:
0
机构:
EMORY UNIV, SCH MED, CTR MOL MED, ATLANTA, GA 30322 USA
EMORY UNIV, SCH MED, CTR MOL MED, ATLANTA, GA 30322 USA
Graham, BH
;
Waymire, KG
论文数:
0
引用数:
0
h-index:
0
机构:
EMORY UNIV, SCH MED, CTR MOL MED, ATLANTA, GA 30322 USA
EMORY UNIV, SCH MED, CTR MOL MED, ATLANTA, GA 30322 USA
Waymire, KG
;
Cottrell, B
论文数:
0
引用数:
0
h-index:
0
机构:
EMORY UNIV, SCH MED, CTR MOL MED, ATLANTA, GA 30322 USA
EMORY UNIV, SCH MED, CTR MOL MED, ATLANTA, GA 30322 USA
Cottrell, B
;
Trounce, IA
论文数:
0
引用数:
0
h-index:
0
机构:
EMORY UNIV, SCH MED, CTR MOL MED, ATLANTA, GA 30322 USA
EMORY UNIV, SCH MED, CTR MOL MED, ATLANTA, GA 30322 USA
Trounce, IA
;
MacGregor, GR
论文数:
0
引用数:
0
h-index:
0
机构:
EMORY UNIV, SCH MED, CTR MOL MED, ATLANTA, GA 30322 USA
EMORY UNIV, SCH MED, CTR MOL MED, ATLANTA, GA 30322 USA
MacGregor, GR
;
Wallace, DC
论文数:
0
引用数:
0
h-index:
0
机构:
EMORY UNIV, SCH MED, CTR MOL MED, ATLANTA, GA 30322 USA
EMORY UNIV, SCH MED, CTR MOL MED, ATLANTA, GA 30322 USA
Wallace, DC
.
NATURE GENETICS,
1997,
16
(03)
:226
-234
[4]
Biochemical evidence for nuclear gene involvement phenotype of non-syndromic deafness associated with mitochondrial 12S rRNA mutation
[J].
Guan, MX
论文数:
0
引用数:
0
h-index:
0
机构:
CALTECH,DIV BIOL,PASADENA,CA 91125
Guan, MX
;
FischelGhodsian, N
论文数:
0
引用数:
0
h-index:
0
机构:
CALTECH,DIV BIOL,PASADENA,CA 91125
FischelGhodsian, N
;
Attardi, G
论文数:
0
引用数:
0
h-index:
0
机构:
CALTECH,DIV BIOL,PASADENA,CA 91125
Attardi, G
.
HUMAN MOLECULAR GENETICS,
1996,
5
(07)
:963
-971
[5]
MITOCHONDRIAL CHLORAMPHENICOL-RESISTANT MUTANTS CAN HAVE DEFICIENCIES IN ENERGY-METABOLISM
[J].
HOWELL, N
论文数:
0
引用数:
0
h-index:
0
HOWELL, N
;
NALTY, MS
论文数:
0
引用数:
0
h-index:
0
NALTY, MS
.
SOMATIC CELL AND MOLECULAR GENETICS,
1988,
14
(02)
:185
-193
[6]
Random genetic drift in the female germline explains the rapid segregation of mammalian mitochondrial DNA
[J].
Jenuth, JP
论文数:
0
引用数:
0
h-index:
0
机构:
MONTREAL NEUROL HOSP & INST, MONTREAL, PQ H3A 2B4, CANADA
Jenuth, JP
;
Peterson, AC
论文数:
0
引用数:
0
h-index:
0
机构:
MONTREAL NEUROL HOSP & INST, MONTREAL, PQ H3A 2B4, CANADA
Peterson, AC
;
Fu, K
论文数:
0
引用数:
0
h-index:
0
机构:
MONTREAL NEUROL HOSP & INST, MONTREAL, PQ H3A 2B4, CANADA
Fu, K
;
Shoubridge, EA
论文数:
0
引用数:
0
h-index:
0
机构:
MONTREAL NEUROL HOSP & INST, MONTREAL, PQ H3A 2B4, CANADA
Shoubridge, EA
.
NATURE GENETICS,
1996,
14
(02)
:146
-151
[7]
ALTERED RIBOSOMAL-RNA GENES IN MITOCHONDRIA FROM MAMMALIAN-CELLS WIT CHLORAMPHENICOL RESISTANCE
[J].
KEARSEY, SE
论文数:
0
引用数:
0
h-index:
0
KEARSEY, SE
;
CRAIG, IW
论文数:
0
引用数:
0
h-index:
0
CRAIG, IW
.
NATURE,
1981,
290
(5807)
:607
-608
[8]
HUMAN-CELLS LACKING MTDNA - REPOPULATION WITH EXOGENOUS MITOCHONDRIA BY COMPLEMENTATION
[J].
KING, MP
论文数:
0
引用数:
0
h-index:
0
KING, MP
;
ATTARDI, G
论文数:
0
引用数:
0
h-index:
0
ATTARDI, G
.
SCIENCE,
1989,
246
(4929)
:500
-503
[9]
DEFECTS IN MITOCHONDRIAL PROTEIN-SYNTHESIS AND RESPIRATORY-CHAIN ACTIVITY SEGREGATE WITH THE TRANSFER RNA(LEU)(UUR) MUTATION ASSOCIATED WITH MITOCHONDRIAL MYOPATHY, ENCEPHALOPATHY, LACTIC-ACIDOSIS, AND STROKE-LIKE EPISODES
[J].
KING, MP
论文数:
0
引用数:
0
h-index:
0
机构:
COLUMBIA UNIV COLL PHYS & SURG,DEPT NEUROL,NEW YORK,NY 10032
KING, MP
;
KOGA, Y
论文数:
0
引用数:
0
h-index:
0
机构:
COLUMBIA UNIV COLL PHYS & SURG,DEPT NEUROL,NEW YORK,NY 10032
KOGA, Y
;
DAVIDSON, M
论文数:
0
引用数:
0
h-index:
0
机构:
COLUMBIA UNIV COLL PHYS & SURG,DEPT NEUROL,NEW YORK,NY 10032
DAVIDSON, M
;
SCHON, EA
论文数:
0
引用数:
0
h-index:
0
机构:
COLUMBIA UNIV COLL PHYS & SURG,DEPT NEUROL,NEW YORK,NY 10032
SCHON, EA
.
MOLECULAR AND CELLULAR BIOLOGY,
1992,
12
(02)
:480
-490
[10]
Laipis P J, 1996, Methods Enzymol, V264, P345, DOI 10.1016/S0076-6879(96)64033-6
←
1
2
→
共 17 条
[1]
EVIDENCE FROM MTDNA SEQUENCES THAT COMMON LABORATORY STRAINS OF INBRED MICE ARE DESCENDED FROM A SINGLE FEMALE
[J].
FERRIS, SD
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF BERKELEY,DEPT BIOCHEM,BERKELEY,CA 94720
FERRIS, SD
;
SAGE, RD
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF BERKELEY,DEPT BIOCHEM,BERKELEY,CA 94720
SAGE, RD
;
WILSON, AC
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF BERKELEY,DEPT BIOCHEM,BERKELEY,CA 94720
WILSON, AC
.
NATURE,
1982,
295
(5845)
:163
-165
[2]
MITOCHONDRIAL RIBOSOMAL-RNA GENE MUTATION IN A PATIENT WITH SPORADIC AMINOGLYCOSIDE OTOTOXICITY
[J].
FISCHELGHODSIAN, N
论文数:
0
引用数:
0
h-index:
0
FISCHELGHODSIAN, N
;
PREZANT, TR
论文数:
0
引用数:
0
h-index:
0
PREZANT, TR
;
BU, XD
论文数:
0
引用数:
0
h-index:
0
BU, XD
;
OZTAS, S
论文数:
0
引用数:
0
h-index:
0
OZTAS, S
.
AMERICAN JOURNAL OF OTOLARYNGOLOGY,
1993,
14
(06)
:399
-403
[3]
A mouse model for mitochondrial myopathy and cardiomyopathy resulting from a deficiency in the heart/muscle isoform of the adenine nucleotide translocator
[J].
Graham, BH
论文数:
0
引用数:
0
h-index:
0
机构:
EMORY UNIV, SCH MED, CTR MOL MED, ATLANTA, GA 30322 USA
EMORY UNIV, SCH MED, CTR MOL MED, ATLANTA, GA 30322 USA
Graham, BH
;
Waymire, KG
论文数:
0
引用数:
0
h-index:
0
机构:
EMORY UNIV, SCH MED, CTR MOL MED, ATLANTA, GA 30322 USA
EMORY UNIV, SCH MED, CTR MOL MED, ATLANTA, GA 30322 USA
Waymire, KG
;
Cottrell, B
论文数:
0
引用数:
0
h-index:
0
机构:
EMORY UNIV, SCH MED, CTR MOL MED, ATLANTA, GA 30322 USA
EMORY UNIV, SCH MED, CTR MOL MED, ATLANTA, GA 30322 USA
Cottrell, B
;
Trounce, IA
论文数:
0
引用数:
0
h-index:
0
机构:
EMORY UNIV, SCH MED, CTR MOL MED, ATLANTA, GA 30322 USA
EMORY UNIV, SCH MED, CTR MOL MED, ATLANTA, GA 30322 USA
Trounce, IA
;
MacGregor, GR
论文数:
0
引用数:
0
h-index:
0
机构:
EMORY UNIV, SCH MED, CTR MOL MED, ATLANTA, GA 30322 USA
EMORY UNIV, SCH MED, CTR MOL MED, ATLANTA, GA 30322 USA
MacGregor, GR
;
Wallace, DC
论文数:
0
引用数:
0
h-index:
0
机构:
EMORY UNIV, SCH MED, CTR MOL MED, ATLANTA, GA 30322 USA
EMORY UNIV, SCH MED, CTR MOL MED, ATLANTA, GA 30322 USA
Wallace, DC
.
NATURE GENETICS,
1997,
16
(03)
:226
-234
[4]
Biochemical evidence for nuclear gene involvement phenotype of non-syndromic deafness associated with mitochondrial 12S rRNA mutation
[J].
Guan, MX
论文数:
0
引用数:
0
h-index:
0
机构:
CALTECH,DIV BIOL,PASADENA,CA 91125
Guan, MX
;
FischelGhodsian, N
论文数:
0
引用数:
0
h-index:
0
机构:
CALTECH,DIV BIOL,PASADENA,CA 91125
FischelGhodsian, N
;
Attardi, G
论文数:
0
引用数:
0
h-index:
0
机构:
CALTECH,DIV BIOL,PASADENA,CA 91125
Attardi, G
.
HUMAN MOLECULAR GENETICS,
1996,
5
(07)
:963
-971
[5]
MITOCHONDRIAL CHLORAMPHENICOL-RESISTANT MUTANTS CAN HAVE DEFICIENCIES IN ENERGY-METABOLISM
[J].
HOWELL, N
论文数:
0
引用数:
0
h-index:
0
HOWELL, N
;
NALTY, MS
论文数:
0
引用数:
0
h-index:
0
NALTY, MS
.
SOMATIC CELL AND MOLECULAR GENETICS,
1988,
14
(02)
:185
-193
[6]
Random genetic drift in the female germline explains the rapid segregation of mammalian mitochondrial DNA
[J].
Jenuth, JP
论文数:
0
引用数:
0
h-index:
0
机构:
MONTREAL NEUROL HOSP & INST, MONTREAL, PQ H3A 2B4, CANADA
Jenuth, JP
;
Peterson, AC
论文数:
0
引用数:
0
h-index:
0
机构:
MONTREAL NEUROL HOSP & INST, MONTREAL, PQ H3A 2B4, CANADA
Peterson, AC
;
Fu, K
论文数:
0
引用数:
0
h-index:
0
机构:
MONTREAL NEUROL HOSP & INST, MONTREAL, PQ H3A 2B4, CANADA
Fu, K
;
Shoubridge, EA
论文数:
0
引用数:
0
h-index:
0
机构:
MONTREAL NEUROL HOSP & INST, MONTREAL, PQ H3A 2B4, CANADA
Shoubridge, EA
.
NATURE GENETICS,
1996,
14
(02)
:146
-151
[7]
ALTERED RIBOSOMAL-RNA GENES IN MITOCHONDRIA FROM MAMMALIAN-CELLS WIT CHLORAMPHENICOL RESISTANCE
[J].
KEARSEY, SE
论文数:
0
引用数:
0
h-index:
0
KEARSEY, SE
;
CRAIG, IW
论文数:
0
引用数:
0
h-index:
0
CRAIG, IW
.
NATURE,
1981,
290
(5807)
:607
-608
[8]
HUMAN-CELLS LACKING MTDNA - REPOPULATION WITH EXOGENOUS MITOCHONDRIA BY COMPLEMENTATION
[J].
KING, MP
论文数:
0
引用数:
0
h-index:
0
KING, MP
;
ATTARDI, G
论文数:
0
引用数:
0
h-index:
0
ATTARDI, G
.
SCIENCE,
1989,
246
(4929)
:500
-503
[9]
DEFECTS IN MITOCHONDRIAL PROTEIN-SYNTHESIS AND RESPIRATORY-CHAIN ACTIVITY SEGREGATE WITH THE TRANSFER RNA(LEU)(UUR) MUTATION ASSOCIATED WITH MITOCHONDRIAL MYOPATHY, ENCEPHALOPATHY, LACTIC-ACIDOSIS, AND STROKE-LIKE EPISODES
[J].
KING, MP
论文数:
0
引用数:
0
h-index:
0
机构:
COLUMBIA UNIV COLL PHYS & SURG,DEPT NEUROL,NEW YORK,NY 10032
KING, MP
;
KOGA, Y
论文数:
0
引用数:
0
h-index:
0
机构:
COLUMBIA UNIV COLL PHYS & SURG,DEPT NEUROL,NEW YORK,NY 10032
KOGA, Y
;
DAVIDSON, M
论文数:
0
引用数:
0
h-index:
0
机构:
COLUMBIA UNIV COLL PHYS & SURG,DEPT NEUROL,NEW YORK,NY 10032
DAVIDSON, M
;
SCHON, EA
论文数:
0
引用数:
0
h-index:
0
机构:
COLUMBIA UNIV COLL PHYS & SURG,DEPT NEUROL,NEW YORK,NY 10032
SCHON, EA
.
MOLECULAR AND CELLULAR BIOLOGY,
1992,
12
(02)
:480
-490
[10]
Laipis P J, 1996, Methods Enzymol, V264, P345, DOI 10.1016/S0076-6879(96)64033-6
←
1
2
→