Subacute sclerosing panencephalitis presenting as acute disseminated encephalomyelitis: A case report

被引:12
作者
Arora, SC
AlTahan, AR
AlZeer, A
AlTahan, F
Ozo, CO
urRahman, N
机构
[1] KING SAUD UNIV, KING KHALID UNIV HOSP, DEPT MED, RIYADH 11472, SAUDI ARABIA
[2] KING FAHAD NATL GUARD HOSP, DEPT RADIOL, RIYADH, SAUDI ARABIA
[3] KING SAUD UNIV, KING KHALID UNIV HOSP, DEPT PATHOL, RIYADH 11472, SAUDI ARABIA
[4] KING SAUD UNIV, KING KHALID UNIV HOSP, DEPT NEUROSURG, RIYADH 11472, SAUDI ARABIA
关键词
subacute sclerosing panencephalitis (SSPE); atypical presentation; acute disseminated encephalo-myelitis (ADEM);
D O I
10.1016/S0022-510X(96)00261-4
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Subacute sclerosing panencephalitis is characterized by the insidious onset of diffuse cerebral dysfunction associated later with myoclonus and typical electroencephalographic changes. The disease progresses relentlessly to coma and death within 2 years. We report a case of acute onset and rapid course associated with atypical CSF, EEG and MRI features simulating acute disseminated encephalomyelitis, Brief review of relevant literature is presented. (C) 1997 Elsevier Science B.V.
引用
收藏
页码:13 / 18
页数:6
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