Dedifferentiated parosteal osteosarcoma with rhabdomyosarcomatous differentiation

被引:12
作者
Reith, JD
Donahue, FI
Hornicek, FJ
机构
[1] Univ Miami, Sch Med, Jackson Mem Med Ctr, Dept Pathol, Miami, FL USA
[2] Univ Miami, Sch Med, Jackson Mem Med Ctr, Dept Radiol, Miami, FL USA
[3] Univ Miami, Sch Med, Dept Orthopaed Surg & Rehabil, Miami, FL USA
关键词
parosteal osteosarcoma; dedifferentiation; rhabdomyosarcoma; femur; MRI;
D O I
10.1007/s002560050557
中图分类号
R826.8 [整形外科学]; R782.2 [口腔颌面部整形外科学]; R726.2 [小儿整形外科学]; R62 [整形外科学(修复外科学)];
学科分类号
摘要
Dedifferentiated parosteal osteosarcomas are characterized histologically by the combination of low-grade fibroblastic osteosarcoma admired with a high-grade component that typically has the appearance of malignant fibrous histiocytoma or osteosarcoma. Herein we report a case of dedifferentiated parosteal osteosarcoma of the distal femur, in which the high-grade component consisted of rhabdomyosarcoma. To our knowledge, a rhabdomyosarcomatous component has not been described previously in a dedifferentiated parosteal osteosarcoma. The clinical, radiologic, and pathologic features of this rare type of surface osteosarcoma are described.
引用
收藏
页码:527 / 531
页数:5
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