Myoclonus in corticobasal degeneration

被引:26
作者
Carella, F [1 ]
Ciano, C [1 ]
Panzica, F [1 ]
Scaioli, V [1 ]
机构
[1] IST NAZL NEUROL C BESTA,DEPT NEUROPHYSIOL,I-20133 MILAN,ITALY
关键词
myoclonus; long-loop responses; corticobasal degeneration; somatosensory evoked potential;
D O I
10.1002/mds.870120419
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Five patients with unilateral myoclonus and a clinical diagnosis of corticobasal degeneration (CBD) were studied. All patients showed enhanced long-loop responses in their myoclonic arms without enlarged somatosensory potentials. The cortical relay time of the long-loop responses was studied in three patients, in two of whom it was <2 ms, even the nonmyoclonic arm. Myoclonus in CBD is probably related to an enhanced long-loop reflex whose pathway is unlikely to be the same as that in classic cortical reflex myoclonus.
引用
收藏
页码:598 / 603
页数:6
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