Common variable immunodeficiency in a patient with systemic lupus erythematosus

被引:19
作者
Swaak, AJG [1 ]
vandenBrink, HG [1 ]
机构
[1] NETHERLANDS RED CROSS,BLOOD TRANSFUS SERV,CENT LAB,DEPT AUTIMMUNE DIS,AMSTERDAM,NETHERLANDS
关键词
systemic lupus erythematosus; common variable immunodeficiency; B cells;
D O I
10.1177/096120339600500314
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
This report describes a young girl who developed systemic lupus erythematosus at the age of 11. In the years thereafter a conversion took place from hypergammaglobulinemia to hypogammaglobulinemia with the absence of circulating and bone marrow B-cells. Some aspects of the aetiopathogenesis of common variable immunodeficiency are discussed.
引用
收藏
页码:242 / 246
页数:5
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