共 16 条
Knocking signalling out of the dystrophin complex
被引:30
作者:

Bredt, DS
论文数: 0 引用数: 0
h-index: 0
机构: Univ Calif San Francisco, Dept Physiol, San Francisco, CA 94143 USA
机构:
[1] Univ Calif San Francisco, Dept Physiol, San Francisco, CA 94143 USA
[2] Univ Calif San Francisco, Sch Med, San Francisco, CA 94143 USA
关键词:
D O I:
10.1038/12085
中图分类号:
Q2 [细胞生物学];
学科分类号:
071009 ;
090102 ;
摘要:
Mice lacking dystrobrevin, a dystrophin-associated protein, exhibit a new form of muscular dystrophy in which the integrity of muscle fibres is maintained, but a component of muscle-cell signalling is disrupted.
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页码:E89 / E91
页数:3
相关论文
共 16 条
[1]
SYNTROPHIN BINDS TO AN ALTERNATIVELY SPLICED EXON OF DYSTROPHIN
[J].
AHN, AH
;
KUNKEL, LM
.
JOURNAL OF CELL BIOLOGY,
1995, 128 (03)
:363-371

AHN, AH
论文数: 0 引用数: 0
h-index: 0
机构: CHILDRENS HOSP,HOWARD HUGHES MED INST,BOSTON,MA 02115

KUNKEL, LM
论文数: 0 引用数: 0
h-index: 0
机构: CHILDRENS HOSP,HOWARD HUGHES MED INST,BOSTON,MA 02115
[2]
Interaction of nitric oxide synthase with the postsynaptic density protein PSD-95 and alpha 1-syntrophin mediated by PDZ domains
[J].
Brenman, JE
;
Chao, DS
;
Gee, SH
;
McGee, AW
;
Craven, SE
;
Santillano, DR
;
Wu, ZQ
;
Huang, F
;
Xia, HH
;
Peters, MF
;
Froehner, SC
;
Bredt, DS
.
CELL,
1996, 84 (05)
:757-767

Brenman, JE
论文数: 0 引用数: 0
h-index: 0
机构: UNIV CALIF SAN FRANCISCO,SCH MED,DEPT PHARMACEUT CHEM,SAN FRANCISCO,CA 94143

Chao, DS
论文数: 0 引用数: 0
h-index: 0
机构: UNIV CALIF SAN FRANCISCO,SCH MED,DEPT PHARMACEUT CHEM,SAN FRANCISCO,CA 94143

Gee, SH
论文数: 0 引用数: 0
h-index: 0
机构: UNIV CALIF SAN FRANCISCO,SCH MED,DEPT PHARMACEUT CHEM,SAN FRANCISCO,CA 94143

McGee, AW
论文数: 0 引用数: 0
h-index: 0
机构: UNIV CALIF SAN FRANCISCO,SCH MED,DEPT PHARMACEUT CHEM,SAN FRANCISCO,CA 94143

Craven, SE
论文数: 0 引用数: 0
h-index: 0
机构: UNIV CALIF SAN FRANCISCO,SCH MED,DEPT PHARMACEUT CHEM,SAN FRANCISCO,CA 94143

Santillano, DR
论文数: 0 引用数: 0
h-index: 0
机构: UNIV CALIF SAN FRANCISCO,SCH MED,DEPT PHARMACEUT CHEM,SAN FRANCISCO,CA 94143

Wu, ZQ
论文数: 0 引用数: 0
h-index: 0
机构: UNIV CALIF SAN FRANCISCO,SCH MED,DEPT PHARMACEUT CHEM,SAN FRANCISCO,CA 94143

Huang, F
论文数: 0 引用数: 0
h-index: 0
机构: UNIV CALIF SAN FRANCISCO,SCH MED,DEPT PHARMACEUT CHEM,SAN FRANCISCO,CA 94143

Xia, HH
论文数: 0 引用数: 0
h-index: 0
机构: UNIV CALIF SAN FRANCISCO,SCH MED,DEPT PHARMACEUT CHEM,SAN FRANCISCO,CA 94143

Peters, MF
论文数: 0 引用数: 0
h-index: 0
机构: UNIV CALIF SAN FRANCISCO,SCH MED,DEPT PHARMACEUT CHEM,SAN FRANCISCO,CA 94143

Froehner, SC
论文数: 0 引用数: 0
h-index: 0
机构: UNIV CALIF SAN FRANCISCO,SCH MED,DEPT PHARMACEUT CHEM,SAN FRANCISCO,CA 94143

Bredt, DS
论文数: 0 引用数: 0
h-index: 0
机构: UNIV CALIF SAN FRANCISCO,SCH MED,DEPT PHARMACEUT CHEM,SAN FRANCISCO,CA 94143
[3]
NITRIC-OXIDE SYNTHASE COMPLEXED WITH DYSTROPHIN AND ABSENT FROM SKELETAL-MUSCLE SARCOLEMMA IN DUCHENNE MUSCULAR-DYSTROPHY
[J].
BRENMAN, JE
;
CHAO, DS
;
XIA, HH
;
ALDAPE, K
;
BREDT, DS
.
CELL,
1995, 82 (05)
:743-752

BRENMAN, JE
论文数: 0 引用数: 0
h-index: 0
机构: UNIV CALIF SAN FRANCISCO,SCH MED,DEPT PATHOL,SAN FRANCISCO,CA 94143

CHAO, DS
论文数: 0 引用数: 0
h-index: 0
机构: UNIV CALIF SAN FRANCISCO,SCH MED,DEPT PATHOL,SAN FRANCISCO,CA 94143

XIA, HH
论文数: 0 引用数: 0
h-index: 0
机构: UNIV CALIF SAN FRANCISCO,SCH MED,DEPT PATHOL,SAN FRANCISCO,CA 94143

ALDAPE, K
论文数: 0 引用数: 0
h-index: 0
机构: UNIV CALIF SAN FRANCISCO,SCH MED,DEPT PATHOL,SAN FRANCISCO,CA 94143

BREDT, DS
论文数: 0 引用数: 0
h-index: 0
机构: UNIV CALIF SAN FRANCISCO,SCH MED,DEPT PATHOL,SAN FRANCISCO,CA 94143
[4]
Selective loss of sarcolemmal nitric oxide synthase in Becker muscular dystrophy
[J].
Chao, DS
;
Gorospe, JRM
;
Brenman, JE
;
Rafael, JA
;
Peters, MF
;
Froehner, SC
;
Hoffman, EP
;
Chamberlain, JS
;
Bredt, DS
.
JOURNAL OF EXPERIMENTAL MEDICINE,
1996, 184 (02)
:609-618

Chao, DS
论文数: 0 引用数: 0
h-index: 0
机构: UNIV CALIF SAN FRANCISCO,SCH MED,DEPT PHYSIOL,SAN FRANCISCO,CA 94143

Gorospe, JRM
论文数: 0 引用数: 0
h-index: 0
机构: UNIV CALIF SAN FRANCISCO,SCH MED,DEPT PHYSIOL,SAN FRANCISCO,CA 94143

Brenman, JE
论文数: 0 引用数: 0
h-index: 0
机构: UNIV CALIF SAN FRANCISCO,SCH MED,DEPT PHYSIOL,SAN FRANCISCO,CA 94143

Rafael, JA
论文数: 0 引用数: 0
h-index: 0
机构: UNIV CALIF SAN FRANCISCO,SCH MED,DEPT PHYSIOL,SAN FRANCISCO,CA 94143

Peters, MF
论文数: 0 引用数: 0
h-index: 0
机构: UNIV CALIF SAN FRANCISCO,SCH MED,DEPT PHYSIOL,SAN FRANCISCO,CA 94143

Froehner, SC
论文数: 0 引用数: 0
h-index: 0
机构: UNIV CALIF SAN FRANCISCO,SCH MED,DEPT PHYSIOL,SAN FRANCISCO,CA 94143

Hoffman, EP
论文数: 0 引用数: 0
h-index: 0
机构: UNIV CALIF SAN FRANCISCO,SCH MED,DEPT PHYSIOL,SAN FRANCISCO,CA 94143

Chamberlain, JS
论文数: 0 引用数: 0
h-index: 0
机构: UNIV CALIF SAN FRANCISCO,SCH MED,DEPT PHYSIOL,SAN FRANCISCO,CA 94143

Bredt, DS
论文数: 0 引用数: 0
h-index: 0
机构: UNIV CALIF SAN FRANCISCO,SCH MED,DEPT PHYSIOL,SAN FRANCISCO,CA 94143
[5]
Role for α-dystrobrevin in the pathogenesis of dystrophin-dependent muscular dystrophies
[J].
Grady, RM
;
Grange, RW
;
Lau, KS
;
Maimone, MM
;
Nichol, MC
;
Stull, JT
;
Sanes, JR
.
NATURE CELL BIOLOGY,
1999, 1 (04)
:215-220

Grady, RM
论文数: 0 引用数: 0
h-index: 0
机构: Washington Univ, Sch Med, Dept Pediat, St Louis, MO 63110 USA

Grange, RW
论文数: 0 引用数: 0
h-index: 0
机构: Washington Univ, Sch Med, Dept Pediat, St Louis, MO 63110 USA

Lau, KS
论文数: 0 引用数: 0
h-index: 0
机构: Washington Univ, Sch Med, Dept Pediat, St Louis, MO 63110 USA

Maimone, MM
论文数: 0 引用数: 0
h-index: 0
机构: Washington Univ, Sch Med, Dept Pediat, St Louis, MO 63110 USA

Nichol, MC
论文数: 0 引用数: 0
h-index: 0
机构: Washington Univ, Sch Med, Dept Pediat, St Louis, MO 63110 USA

Stull, JT
论文数: 0 引用数: 0
h-index: 0
机构: Washington Univ, Sch Med, Dept Pediat, St Louis, MO 63110 USA

Sanes, JR
论文数: 0 引用数: 0
h-index: 0
机构: Washington Univ, Sch Med, Dept Pediat, St Louis, MO 63110 USA
[6]
MUTATIONS IN THE LAMININ ALPHA-2-CHAIN GENE (LAMA2) CAUSE MEROSIN-DEFICIENT CONGENITAL MUSCULAR-DYSTROPHY
[J].
HELBLINGLECLERC, A
;
ZHANG, X
;
TOPALOGLU, H
;
CRUAUD, C
;
TESSON, F
;
WEISSENBACH, J
;
TOME, FMS
;
SCHWARTZ, K
;
FARDEAU, M
;
TRYGGVASON, K
;
GUICHENEY, P
.
NATURE GENETICS,
1995, 11 (02)
:216-218

HELBLINGLECLERC, A
论文数: 0 引用数: 0
h-index: 0
机构: UNIV OULU,DEPT BIOCHEM,SF-90571 OULU,FINLAND

ZHANG, X
论文数: 0 引用数: 0
h-index: 0
机构: UNIV OULU,DEPT BIOCHEM,SF-90571 OULU,FINLAND

TOPALOGLU, H
论文数: 0 引用数: 0
h-index: 0
机构: UNIV OULU,DEPT BIOCHEM,SF-90571 OULU,FINLAND

CRUAUD, C
论文数: 0 引用数: 0
h-index: 0
机构: UNIV OULU,DEPT BIOCHEM,SF-90571 OULU,FINLAND

TESSON, F
论文数: 0 引用数: 0
h-index: 0
机构: UNIV OULU,DEPT BIOCHEM,SF-90571 OULU,FINLAND

WEISSENBACH, J
论文数: 0 引用数: 0
h-index: 0
机构: UNIV OULU,DEPT BIOCHEM,SF-90571 OULU,FINLAND

TOME, FMS
论文数: 0 引用数: 0
h-index: 0
机构: UNIV OULU,DEPT BIOCHEM,SF-90571 OULU,FINLAND

SCHWARTZ, K
论文数: 0 引用数: 0
h-index: 0
机构: UNIV OULU,DEPT BIOCHEM,SF-90571 OULU,FINLAND

FARDEAU, M
论文数: 0 引用数: 0
h-index: 0
机构: UNIV OULU,DEPT BIOCHEM,SF-90571 OULU,FINLAND

论文数: 引用数:
h-index:
机构:

GUICHENEY, P
论文数: 0 引用数: 0
h-index: 0
机构: UNIV OULU,DEPT BIOCHEM,SF-90571 OULU,FINLAND
[7]
Unexpected modes of PDZ domain scaffolding revealed by structure of nNOS-syntrophin complex
[J].
Hillier, BJ
;
Christopherson, KS
;
Prehoda, KE
;
Bredt, DS
;
Lim, WA
.
SCIENCE,
1999, 284 (5415)
:812-815

Hillier, BJ
论文数: 0 引用数: 0
h-index: 0
机构: Univ Calif San Francisco, Dept Mol & Cellular Pharmacol, San Francisco, CA 94143 USA

Christopherson, KS
论文数: 0 引用数: 0
h-index: 0
机构: Univ Calif San Francisco, Dept Mol & Cellular Pharmacol, San Francisco, CA 94143 USA

Prehoda, KE
论文数: 0 引用数: 0
h-index: 0
机构: Univ Calif San Francisco, Dept Mol & Cellular Pharmacol, San Francisco, CA 94143 USA

Bredt, DS
论文数: 0 引用数: 0
h-index: 0
机构: Univ Calif San Francisco, Dept Mol & Cellular Pharmacol, San Francisco, CA 94143 USA

Lim, WA
论文数: 0 引用数: 0
h-index: 0
机构:
Univ Calif San Francisco, Dept Mol & Cellular Pharmacol, San Francisco, CA 94143 USA Univ Calif San Francisco, Dept Mol & Cellular Pharmacol, San Francisco, CA 94143 USA
[8]
The sarcoglycan complex in limb-girdle muscular dystrophy
[J].
Lim, LE
;
Campbell, KP
.
CURRENT OPINION IN NEUROLOGY,
1998, 11 (05)
:443-452

Lim, LE
论文数: 0 引用数: 0
h-index: 0
机构: Univ Iowa, Coll Med, Howard Hughes Med Inst, Dept Physiol & Biophys, Iowa City, IA 52242 USA

Campbell, KP
论文数: 0 引用数: 0
h-index: 0
机构:
Univ Iowa, Coll Med, Howard Hughes Med Inst, Dept Physiol & Biophys, Iowa City, IA 52242 USA Univ Iowa, Coll Med, Howard Hughes Med Inst, Dept Physiol & Biophys, Iowa City, IA 52242 USA
[9]
Dystrobrevin deficiency at the sarcolemma of patients with muscular dystrophy
[J].
Metzinger, L
;
Blake, DJ
;
Squier, MV
;
Anderson, LVB
;
Deconinck, AE
;
Nawrotzki, R
;
HiltonJones, D
;
Davies, KE
.
HUMAN MOLECULAR GENETICS,
1997, 6 (07)
:1185-1191

Metzinger, L
论文数: 0 引用数: 0
h-index: 0
机构: UNIV OXFORD,DEPT BIOCHEM,GENET UNIT,OXFORD OX1 3QU,ENGLAND

Blake, DJ
论文数: 0 引用数: 0
h-index: 0
机构: UNIV OXFORD,DEPT BIOCHEM,GENET UNIT,OXFORD OX1 3QU,ENGLAND

Squier, MV
论文数: 0 引用数: 0
h-index: 0
机构: UNIV OXFORD,DEPT BIOCHEM,GENET UNIT,OXFORD OX1 3QU,ENGLAND

Anderson, LVB
论文数: 0 引用数: 0
h-index: 0
机构: UNIV OXFORD,DEPT BIOCHEM,GENET UNIT,OXFORD OX1 3QU,ENGLAND

Deconinck, AE
论文数: 0 引用数: 0
h-index: 0
机构: UNIV OXFORD,DEPT BIOCHEM,GENET UNIT,OXFORD OX1 3QU,ENGLAND

Nawrotzki, R
论文数: 0 引用数: 0
h-index: 0
机构: UNIV OXFORD,DEPT BIOCHEM,GENET UNIT,OXFORD OX1 3QU,ENGLAND

HiltonJones, D
论文数: 0 引用数: 0
h-index: 0
机构: UNIV OXFORD,DEPT BIOCHEM,GENET UNIT,OXFORD OX1 3QU,ENGLAND

Davies, KE
论文数: 0 引用数: 0
h-index: 0
机构: UNIV OXFORD,DEPT BIOCHEM,GENET UNIT,OXFORD OX1 3QU,ENGLAND
[10]
ISOLATION OF CANDIDATE CDNAS FOR PORTIONS OF THE DUCHENNE MUSCULAR-DYSTROPHY GENE
[J].
MONACO, AP
;
NEVE, RL
;
COLLETTIFEENER, C
;
BERTELSON, CJ
;
KURNIT, DM
;
KUNKEL, LM
.
NATURE,
1986, 323 (6089)
:646-650

MONACO, AP
论文数: 0 引用数: 0
h-index: 0
机构: HARVARD UNIV, CHILDRENS HOSP,SCH MED,DEPT PEDIAT, MENTAL RETARDAT PROGRAM,DIV GENET, BOSTON, MA 02115 USA

NEVE, RL
论文数: 0 引用数: 0
h-index: 0
机构: HARVARD UNIV, CHILDRENS HOSP,SCH MED,DEPT PEDIAT, MENTAL RETARDAT PROGRAM,DIV GENET, BOSTON, MA 02115 USA

COLLETTIFEENER, C
论文数: 0 引用数: 0
h-index: 0
机构: HARVARD UNIV, CHILDRENS HOSP,SCH MED,DEPT PEDIAT, MENTAL RETARDAT PROGRAM,DIV GENET, BOSTON, MA 02115 USA

BERTELSON, CJ
论文数: 0 引用数: 0
h-index: 0
机构: HARVARD UNIV, CHILDRENS HOSP,SCH MED,DEPT PEDIAT, MENTAL RETARDAT PROGRAM,DIV GENET, BOSTON, MA 02115 USA

KURNIT, DM
论文数: 0 引用数: 0
h-index: 0
机构: HARVARD UNIV, CHILDRENS HOSP,SCH MED,DEPT PEDIAT, MENTAL RETARDAT PROGRAM,DIV GENET, BOSTON, MA 02115 USA

KUNKEL, LM
论文数: 0 引用数: 0
h-index: 0
机构: HARVARD UNIV, CHILDRENS HOSP,SCH MED,DEPT PEDIAT, MENTAL RETARDAT PROGRAM,DIV GENET, BOSTON, MA 02115 USA