Surgical correction of craniosynostosis in malignant osteopetrosis

被引:12
作者
Krimmel, M
Niemann, G
Will, B
Reinert, S
机构
[1] Univ Hosp Tubingen, Dept Neurosurg, Tubingen, Germany
[2] Univ Hosp Tubingen, Dept Pediat, Tubingen, Germany
[3] Univ Hosp Tubingen, Dept Oral & Maxillofacial Plast Surg, Tubingen, Germany
关键词
osteopetrosis; craniosynostosis;
D O I
10.1097/00001665-200403000-00007
中图分类号
R61 [外科手术学];
学科分类号
摘要
In osteopetrosis, bone healing is complicated by progressive sclerosis. A 2-year-old blind boy with malignant osteopetrosis developed increased intracranial pressure secondary to craniosynostosis. Osteopetrosis had already been treated with bone marrow transplantation (BMT), and bone remodeling seemed to be restored. A craniotomy was performed. The postoperative course and bone healing were uneventful. After successful BMT, craniofacial procedures seem to be possible without a high risk for osteomyelitis.
引用
收藏
页码:218 / 220
页数:3
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