Congenital cystic adenomatoid malformation of the lung associated with esophageal atresia and tracheoesophageal fistula

被引:9
作者
De Felice, C [1 ]
Di Maggio, G [1 ]
Messina, M [1 ]
Toti, P [1 ]
Bagnoli, F [1 ]
Bracci, R [1 ]
Tota, G [1 ]
机构
[1] Univ Siena, Inst Prevent Pediat & Neonatol, I-53100 Siena, Italy
关键词
esophageal atresia; tracheoesophageal fistula; congenital cystic adenomatoid malformation pneumothorax; newborn;
D O I
10.1007/s003830050571
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Bronchopulmonary malformations associated with esophageal atresia (EA) and tracheoesophageal fistula (TEF) are extremely rare. The authors describe a case-of type II congenital cystic adenomatoid malformation (CCAM) of the right lower lobe associated with EA and TEF(Vogt-Gross type C) in a full-term female infant. The CCAM presented as an incidental radiologic finding, and a contralateral tension pneumothorax developed shortly after surgical repair of the EA. Early recognition of this rare association is essential for correct operative management.
引用
收藏
页码:260 / 263
页数:4
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