Localized lipoatrophia with persistent circulating autoantibodies and partial immunoglobulin A deficiency in a child

被引:14
作者
TremeauMartinage, C [1 ]
BayleLebey, P [1 ]
Grouteau, E [1 ]
Bazex, J [1 ]
机构
[1] CHU PURPAN,DEPT PEDIAT,F-31059 TOULOUSE,FRANCE
关键词
localized lipoatrophia; lipodystrophia centrifugalis abdominalis infantilis; connective tissue panniculitis; antinuclear antibodies;
D O I
10.1159/000246412
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
A 7-year-old Caucasian girl developed lipoatrophic areas on the abdomen and left thigh. Laboratory tests showed a partial IgA deficiency, circulating autoantibodies (ANAs, double- and single-stranded anti-DNAs, rheumatoid factor). The clinical aspect resembles lipodystrophia centrifugalis abdominalis infantilis, but autoimmune abnormalities suggest connective tissue panniculitis which underlines the overlap between the different forms of localized lipoatrophias.
引用
收藏
页码:353 / 357
页数:5
相关论文
共 22 条
[1]   ASSOCIATION OF PARTIAL LIPODYSTROPHY AND SJOGRENS SYNDROME [J].
ALARCONSEGOVIA, D ;
RAMOSNIEMBRO, F .
ANNALS OF INTERNAL MEDICINE, 1976, 85 (04) :474-475
[2]   LIPOATROPHIC PANNICULITIS - A POSSIBLE AUTOIMMUNE INFLAMMATORY DISEASE OF FAT - REPORT OF 3 CASES [J].
BILLINGS, JK ;
MILGRAUM, SS ;
GUPTA, AK ;
HEADINGTON, JT ;
RASMUSSEN, JE .
ARCHIVES OF DERMATOLOGY, 1987, 123 (12) :1662-1666
[3]  
CAPUTO R, 1995, LIPOATROPHY PEDIATR, V3, P221
[4]   SIGNIFICANCE OF A POSITIVE ANTI-NUCLEAR ANTIBODY-TEST IN A PEDIATRIC POPULATION [J].
CHUDWIN, DS ;
AMMANN, AJ ;
COWAN, MJ ;
WARA, DW .
AMERICAN JOURNAL OF DISEASES OF CHILDREN, 1983, 137 (11) :1103-1106
[5]   CUTANEOUS AND SUBCUTANEOUS INFLAMMATORY SCLEROSIS SYNDROMES [J].
DOYLE, JA ;
CONNOLLY, SM ;
WINKELMANN, RK .
ARCHIVES OF DERMATOLOGY, 1982, 118 (11) :886-890
[6]   LUPUS PROFUNDUS IN CHILDREN - TREATMENT WITH HYDROXYCHLOROQUINE [J].
FOX, JN ;
KLAPMAN, MH ;
ROWE, L .
JOURNAL OF THE AMERICAN ACADEMY OF DERMATOLOGY, 1987, 16 (04) :839-844
[7]   MULTIPLE AREAS OF LOCALIZED TISSUE LOSS IN A CHILD [J].
GUPTA, AK ;
RASMUSSEN, JE .
ARCHIVES OF DERMATOLOGY, 1986, 122 (10) :1199-+
[8]   GENERALIZED LIPODYSTROPHY, SCLERODERMA, AND HODGKINS-DISEASE [J].
HALL, SW ;
GILLESPIE, JJ ;
TENCZYNSKI, TF .
ARCHIVES OF INTERNAL MEDICINE, 1978, 138 (08) :1303-1304
[9]   LIPODYSTROPHIA CENTRIFUGALIS ABDOMINALIS INFANTILIS OCCURRING IN THE NECK [J].
HIGUCHI, T ;
YAMAKAGE, A ;
TAMURA, T ;
MIYACHI, Y .
DERMATOLOGY, 1994, 188 (02) :142-144
[10]   LIPODYSTROPHIA CENTRIFUGALIS ABDOMINALIS INFANTILIS - A FOLLOW-UP-STUDY [J].
IMAMURA, S ;
YAMADA, M ;
YAMAMOTO, K .
JOURNAL OF THE AMERICAN ACADEMY OF DERMATOLOGY, 1984, 11 (02) :203-209