Guidelines for the management of hemophilia

被引：1440

作者：

Srivastava, A. ^{[1
]}

Brewer, A. K. ^{[2
]}

Mauser-Bunschoten, E. P. ^{[3
,4
]}

Key, N. S. ^{[5
]}

Kitchen, S. ^{[6
]}

Llinas, A. ^{[7
,8
,9
]}

Ludlam, C. A. ^{[10
]}

Mahlangu, J. N. ^{[11
,12
,13
]}

Mulder, K. ^{[14
]}

Poon, M. C. ^{[15
,16
,17
,18
,19
]}

Street, A. ^{[20
]}

机构：

[1] Christian Med Coll & Hosp, Dept Hematol, Vellore 632004, Tamil Nadu, India

[2] Royal Infirm, Dept Oral Surg, Glasgow G31 2ER, Lanark, Scotland

[3] Univ Med Ctr Utrecht, Van Creveldklin, Utrecht, Netherlands

[4] Univ Med Ctr Utrecht, Dept Hematol, Utrecht, Netherlands

[5] Univ N Carolina, Dept Med, Chapel Hill, NC USA

[6] Royal Hallamshire Hosp, Sheffield Haemophilia & Thrombosis Ctr, Sheffield S10 2JF, S Yorkshire, England

[7] Fdn Santa Fe Univ Hosp Fdn Cosme & Damian, Dept Orthopaed & Traumatol, Bogota, Colombia

[8] Univ Los Andes, Bogota, Colombia

[9] Univ Rosario, Bogota, Colombia

[10] Royal Infirm, Comprehens Care Haemophilia & Thrombosis Ctr, Edinburgh, Midlothian, Scotland

[11] Johannesburg Hosp, Haemophilia Comprehens Care Ctr, Johannesburg, South Africa

[12] Natl Hlth Lab Serv, Fac Hlth Sci, Dept Mol Med & Haematol, Johannesburg, South Africa

[13] Univ Witwatersrand, Johannesburg, South Africa

[14] Hlth Sci Ctr, Bleeding Disorders Clin, Winnipeg, MB, Canada

[15] Univ Calgary, Dept Med, Foothills Hosp, Calgary, AB, Canada

[16] Univ Calgary, Dept Pediat, Foothills Hosp, Calgary, AB T2N 1N4, Canada

[17] Univ Calgary, Dept Oncol, Foothills Hosp, Calgary, AB, Canada

[18] Univ Calgary, Foothills Hosp, So Alberta Rare Blood & Bleeding Disorders Compre, Calgary, AB, Canada

[19] Calgary Hlth Reg, Calgary, AB, Canada

[20] Alfred Hosp, Melbourne, Vic, Australia

来源：

HAEMOPHILIA | 2013年 / 19卷 / 01期

关键词：

bleeding disorders; guidelines; hemophilia; management; treatment; IMMUNE TOLERANCE INDUCTION; TOTAL KNEE ARTHROPLASTY; HEPATITIS-B-VACCINE; QUALITY-OF-LIFE; FACTOR-VIII CONCENTRATE; ISCHEMIC-HEART-DISEASE; VON-WILLEBRAND-DISEASE; FRESH-FROZEN PLASMA; TERM-FOLLOW-UP; BLEEDING DISORDERS;

D O I：

10.1111/j.1365-2516.2012.02909.x

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Hemophilia is a rare disorder that is complex to diagnose and to manage. These evidence-based guidelines offer practical recommendations on the diagnosis and general management of hemophilia, as well as the management of complications including musculoskeletal issues, inhibitors, and transfusion-transmitted infections. By compiling these guidelines, the World Federation of Hemophilia aims to assist healthcare providers seeking to initiate and/or maintain hemophilia care programs, encourage practice harmonization around the world and, where recommendations lack adequate evidence, stimulate appropriate studies.

引用

页码：E1 / E47

页数：47

共 282 条

[1]

Adcock DMHD, 2008, Collection, transport, and processing of blood specimens for testing plasma-based coagulation assays and molecular hemostasis assays

[2]

approved Guideline, V5th, DOI DOI 10.1177/0004563216665868

[3] Rheumatological management of patients with hemophilia. Part II: Muscle hematomas and pseudotumors [J].

Alcalay, M ;

Deplas, A .

JOINT BONE SPINE, 2002, 69 (06) :556-559

[4]

[Anonymous], 2008, H47A2 CLSI

[5]

[Anonymous], 2011, OR HLTH MAN PAT PRES

[6]

[Anonymous], 2012, JTH IN PRESS

[7] Mortality rates and causes of death among all HIV-positive individuals with hemophilia in Canada over 21 years of follow-up [J].

Arnold, Donald M. ;

Julian, Jim A. ;

Walker, Irwin R. .

BLOOD, 2006, 108 (02) :460-464

[8] HEMOPHILIC ARTHROPATHY - CURRENT CONCEPTS OF PATHOGENESIS AND MANAGEMENT [J].

ARNOLD, WD ;

HILGARTNER, MW .

JOURNAL OF BONE AND JOINT SURGERY-AMERICAN VOLUME, 1977, 59 (03) :287-305

[9] THE CLINICAL-FEATURES OF EARLY BLEEDING INTO THE MUSCLES OF THE LOWER-LIMB IN SEVERE HEMOPHILIACS [J].

ARONSTAM, A ;

BROWNE, RS ;

WASSEF, M ;

HAMAD, Z .

JOURNAL OF BONE AND JOINT SURGERY-BRITISH VOLUME, 1983, 65 (01) :19-23

[10]

ARONSTAM A, 1983, CLIN LAB HAEMATOL, V5, P157

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