Pseudohypo-aldosteronism and cholelithiasis: Coincidence or pathogenetic correlation?

被引:15
作者
Akkurt, I [1 ]
Kuhnle, U [1 ]
Ringenberg, C [1 ]
机构
[1] UNIV MUNICH, CHILDRENS HOSP, D-8000 MUNICH, GERMANY
关键词
cholelithiasis; pseudohypo-aldosteronism; dehydration; salt-wasting; infant;
D O I
10.1007/s004310050615
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Cholelithiasis is being documented with increasing frequency in the paediatric age group. Causes of gallstone formation in infants and neonates seem to differ from those in older children and adolescents, Two infants with pseudohypo-aldosteronism and cholelithiasis are reported, Salt-wasting and dehydration in pseudohypo-aldosteronism are suggested to be the pathogenetic mechanisms leading to gallstone formation possibly beginning in fetal life. The diagnosis of pseudohypo-aldosteronism may be missed, when salt-wasting is transitional. Cholelithiasis may go undetected when asymptomatic. Conclusion Pseudohypo-aldosteronism should be considered in infants with cholelithiasis even without obvious salt-wasting signs, Routine ultrasonographic screening for gallstones should be performed in patients with pseudohypo-aldosteronism.
引用
收藏
页码:363 / 366
页数:4
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