Prion diseases

被引:83
作者
Knight, RSG [1 ]
Will, RG [1 ]
机构
[1] Western Gen Hosp, Natl CJD Surveillance Unit, Edinburgh EH4 2XU, Midlothian, Scotland
关键词
D O I
10.1136/jnnp.2004.036137
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Prion diseases or transmissible spongiform encephalopathies (table 1) are characterised by the deposition of PrPSc, an abnormal form of a normal cellular protein, PrPC. These diseases exist in sporadic (idiopathic), genetic, and acquired forms.
引用
收藏
页码:I36 / I42
页数:7
相关论文
共 5 条
[1]   Iatrogenic Creutzfeldt-Jakob disease at the millennium [J].
Brown, P ;
Preece, M ;
Brandel, JP ;
Sato, T ;
McShane, L ;
Zerr, I ;
Fletcher, A ;
Will, RG ;
Pocchiari, M ;
Cashman, NR ;
d'Aignaux, JH ;
Cervenáková, L ;
Fradkin, J ;
Schonberger, LB ;
Collins, SJ .
NEUROLOGY, 2000, 55 (08) :1075-1081
[2]   MRI of Creutzfeldt-Jakob disease: Imaging features and recommended MRI protocol [J].
Collie, DA ;
Sellar, RJ ;
Zeidler, M ;
Colchester, ACF ;
Knight, R ;
Will, RG .
CLINICAL RADIOLOGY, 2001, 56 (09) :726-739
[3]   Mutations of the prion protein gene -: Phenotypic spectrum [J].
Kovács, GG ;
Trabattoni, G ;
Hainfellner, JA ;
Ironside, JW ;
Knight, RSG ;
Budka, H .
JOURNAL OF NEUROLOGY, 2002, 249 (11) :1567-1582
[4]  
Will RG, 2000, ANN NEUROL, V47, P575
[5]  
Will RG, 1999, COLD SPRING HARBOR M, V38, P465