Hereditary haemorrhagic telangiectasia and pulmonary arteriovenous malformations: issues in clinical management and review of pathogenic mechanisms

被引:281
作者
Shovlin, CL
Letarte, M
机构
[1] Hammersmith Hosp, Natl Heart & Lung Inst, Imperial Coll, Sch Med, London W12 0NN, England
[2] Hosp Sick Children, Canc & Blood Programme, Toronto, ON M5G 1X8, Canada
基金
英国惠康基金;
关键词
D O I
10.1136/thx.54.8.714
中图分类号
R56 [呼吸系及胸部疾病];
学科分类号
摘要
[No abstract available]
引用
收藏
页码:714 / 729
页数:16
相关论文
共 195 条
  • [1] Expression of endoglin mRNA and protein in human vascular smooth muscle cells
    Adam, PJ
    Clesham, GJ
    Weissberg, PL
    [J]. BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1998, 247 (01) : 33 - 37
  • [2] ANABTAWI I N, 1965, Ann Thorac Surg, V1, P277
  • [3] Embolotherapy for pulmonary arteriovenous malformations in patients with hereditary hemorrhagic telangiectasia (Rendu-Osler-Weber syndrome)
    Andersen, PE
    Kjeldsen, AD
    Oxhoj, H
    Vase, P
    White, RI
    [J]. ACTA RADIOLOGICA, 1998, 39 (06) : 723 - 726
  • [4] HEMODYNAMICS AND GAS-EXCHANGE BEFORE AND AFTER COIL EMBOLIZATION OF PULMONARY ARTERIOVENOUS-MALFORMATIONS
    ANDRIVET, P
    LOFASO, F
    CARETTE, MF
    ALLEGRINI, J
    ADNOT, S
    [J]. EUROPEAN RESPIRATORY JOURNAL, 1995, 8 (07) : 1228 - 1230
  • [5] EXPRESSION AND SECRETION OF TYPE-BETA TRANSFORMING GROWTH-FACTOR BY ACTIVATED HUMAN MACROPHAGES
    ASSOIAN, RK
    FLEURDELYS, BE
    STEVENSON, HC
    MILLER, PJ
    MADTES, DK
    RAINES, EW
    ROSS, R
    SPORN, MB
    [J]. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1987, 84 (17) : 6020 - 6024
  • [6] IDENTIFICATION OF HUMAN ACTIVIN AND TGF-BETA TYPE-I RECEPTORS THAT FORM HETEROMERIC KINASE COMPLEXES WITH TYPE-II RECEPTORS
    ATTISANO, L
    CARCAMO, J
    VENTURA, F
    WEIS, FMB
    MASSAGUE, J
    WRANA, JL
    [J]. CELL, 1993, 75 (04) : 671 - 680
  • [7] EMBOLOTHERAPY OF PULMONARY ARTERIOVENOUS-MALFORMATIONS WITH DETACHABLE BALLOONS
    BARTH, KH
    WHITE, RI
    KAUFMAN, SL
    TERRY, PB
    ROLAND, JM
    [J]. RADIOLOGY, 1982, 142 (03) : 599 - 606
  • [8] 2-DIMENSIONAL CONTRAST ECHOCARDIOGRAPHY IN THE DETECTION AND FOLLOW-UP OF CONGENITAL PULMONARY ARTERIOVENOUS-MALFORMATIONS
    BARZILAI, B
    WAGGONER, AD
    SPESSERT, C
    PICUS, D
    GOODENBERGER, D
    [J]. AMERICAN JOURNAL OF CARDIOLOGY, 1991, 68 (15) : 1507 - 1510
  • [9] LIVER-TRANSPLANTATION FOR HEPATIC ARTERIOVENOUS MALFORMATION IN HEREDITARY HEMORRHAGIC TELANGIECTASIA
    BAUER, T
    BRITTON, P
    LOMAS, D
    WIGHT, DGD
    FRIEND, PJ
    ALEXANDER, GJM
    [J]. JOURNAL OF HEPATOLOGY, 1995, 22 (05): : 586 - 590
  • [10] BEAN W B, 1960, Arch Intern Med, V106, P35