Is ALS a systemic disorder? Evidence from muscle mitochondria

被引:20
作者
Appel, SH [1 ]
机构
[1] Methodist Neurol Inst, Dept Neurol, Houston, TX 77030 USA
关键词
D O I
10.1016/j.expneurol.2005.12.025
中图分类号
Q189 [神经科学];
学科分类号
071006 [神经生物学];
摘要
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页码:1 / 3
页数:3
相关论文
共 29 条
[1]
Early vacuolization and mitochondrial damage in motor neurons of FALS mice are not associated with apoptosis or with changes in cytochrome oxidase histochemical reactivity [J].
Bendotti, C ;
Calvaresi, N ;
Chiveri, L ;
Prelle, A ;
Moggio, M ;
Braga, M ;
Silani, V ;
De Biasi, S .
JOURNAL OF THE NEUROLOGICAL SCIENCES, 2001, 191 (1-2) :25-33
[2]
Increased oxidative damage to DNA in ALS patients [J].
Bogdanov, M ;
Brown, RH ;
Matson, W ;
Smart, R ;
Hayden, D ;
O'Donnell, H ;
Beal, MF ;
Cudkowicz, M .
FREE RADICAL BIOLOGY AND MEDICINE, 2000, 29 (07) :652-658
[3]
Borthwick GM, 1999, ANN NEUROL, V46, P787, DOI 10.1002/1531-8249(199911)46:5<787::AID-ANA17>3.0.CO
[4]
2-8
[5]
BRADLEY LJ, 2003, AMYOTROPH LATERAL SC, V4, P87
[6]
Cytochrome c oxidase subunit I microdeletion in a patient with motor neuron disease [J].
Comi, GP ;
Bordoni, A ;
Salani, S ;
Franceschina, L ;
Sciacco, M ;
Prelle, A ;
Fortunato, F ;
Zeviani, M ;
Napoli, L ;
Bresolin, N ;
Moggio, M ;
Ausenda, CD ;
Taanman, JW ;
Scarlato, G .
ANNALS OF NEUROLOGY, 1998, 43 (01) :110-116
[7]
Amyotrophic lateral sclerosis: Oxidative energy metabolism and calcium homeostasis in peripheral blood lymphocytes [J].
Curti, D ;
Malaspina, A ;
Facchetti, G ;
Camana, C ;
Mazzini, L ;
Tosca, P ;
Zerbi, F ;
Ceroni, M .
NEUROLOGY, 1996, 47 (04) :1060-1064
[8]
Up-regulation of mitochondrial uncoupling protein 3 reveals an early muscular metabolic defect in amyotrophic lateral sclerosis [J].
Dupuis, L ;
di Scala, F ;
Rene, F ;
de Tapia, M ;
Oudart, H ;
Pradat, PF ;
Meininger, V ;
Loeffler, JP .
FASEB JOURNAL, 2003, 17 (12) :2091-+
[9]
Is there mitochondrial dysfunction in amyotrophic lateral sclerosis skeletal muscle? Reply [J].
Echaniz-Laguna, A ;
Zoll, J ;
Ribera, F ;
Tranchant, C ;
Warter, JM ;
Lonsdorfer, J ;
Lampert, E .
ANNALS OF NEUROLOGY, 2003, 53 (05) :687-688
[10]
Mitochondrial respiratory chain function in skeletal muscle of ALS patients [J].
Echaniz-Laguna, A ;
Zoll, J ;
Ribera, F ;
Tranchant, C ;
Warter, JM ;
Lonsdorfer, J ;
Lampert, E .
ANNALS OF NEUROLOGY, 2002, 52 (05) :623-627