Primary epithelioid angiosarcoma of the lung presenting as pulmonary hemorrhage

被引:44
作者
Sheppard, MN
Hansell, DM
DuBois, RM
Nicholson, AG
机构
[1] ROYAL BROMPTON NATL HEART & LUNG HOSP,DEPT HISTOPATHOL,LONDON SW3 6NP,ENGLAND
[2] ROYAL BROMPTON NATL HEART & LUNG HOSP,DEPT RADIOL,LONDON SW3 6NP,ENGLAND
[3] ROYAL BROMPTON NATL HEART & LUNG HOSP,DEPT RESP MED,LONDON SW3 6NP,ENGLAND
关键词
lung; angiosarcoma; epithelioid angiosarcoma;
D O I
10.1016/S0046-8177(97)90140-4
中图分类号
R36 [病理学];
学科分类号
100104 ;
摘要
Pulmonary angiosarcomas are usually secondary tumors, and only a few primary cases have been described. We report a unique case of epithelioid angiosarcoma arising in the lungs as a bilateral multinodular infiltrate and presenting as pulmonary hemorrhage. Because of its epithelioid histology, this tumor may resemble a carcinoma, also staining positively for keratin markers, Therefore, unless the diagnosis of epithelioid angiosarcoma is considered and endothelial markers used, the diagnosis of epithelioid angiosarcoma may be overlooked at this site. Copyright (C) 1997 by W.B. Saunders Company.
引用
收藏
页码:383 / 385
页数:3
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