Cystic Fibrosis Foundation Evidence-Based Guidelines for Management of Infants with Cystic Fibrosis

被引：302

作者：

Borowitz, Drucy ^{[1
]}

Robinson, Karen A. ^{[2
]}

Rosenfeld, Margaret ^{[4
]}

Davis, Stephanie D. ^{[5
]}

Sabadosa, Kathryn A. ^{[6
]}

Spear, Stephanie L. ^{[7
]}

Michel, Suzanne H. ^{[8
]}

Parad, Richard B. ^{[9
]}

White, Terry B. ^{[3
]}

Farrell, Philip M. ^{[10
]}

Marshall, Bruce C. ^{[3
]}

Accurso, Frank J. ^{[11
]}

机构：

[1] SUNY Buffalo, Womens & Childrens Hosp Buffalo, Buffalo, NY 14260 USA

[2] Johns Hopkins Sch Med, Baltimore, MD USA

[3] Cyst Fibrosis Fdn, Bethesda, MD 20814 USA

[4] Univ Washington, Seattle, WA 98195 USA

[5] Univ N Carolina, Chapel Hill, NC USA

[6] Dartmouth Coll, Hanover, NH 03755 USA

[7] Cincinnati Childrens Hosp Med Ctr, Cincinnati, OH USA

[8] Childrens Hosp Philadelphia, Philadelphia, PA 19104 USA

[9] Brigham & Womens Hosp, Boston, MA 02115 USA

[10] Univ Wisconsin, Sch Med & Publ Hlth, Madison, WI USA

[11] Childrens Hosp, Denver, CO 80218 USA

来源：

JOURNAL OF PEDIATRICS | 2009年 / 155卷 / 06期

关键词：

RESPIRATORY SYNCYTIAL VIRUS; PSEUDOMONAS-AERUGINOSA COLONIZATION; PANCREATIC-ENZYME SUPPLEMENTS; INHALED HYPERTONIC SALINE; SOLUBLE VITAMIN STATUS; YOUNG-CHILDREN; LUNG-FUNCTION; PULMONARY-FUNCTION; COMPUTED-TOMOGRAPHY; AIRWAY FUNCTION;

D O I：

10.1016/j.jpeds.2009.09.001

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

Newborn screening for cystic fibrosis (CF) offers the opportunity for early medical and nutritional intervention that can lead to improved outcomes. Management of the asymptomatic infant diagnosed with CF through newborn screening, prenatal diagnosis, or sibling screening is different from treatment of the symptomatically diagnosed individual. The focus of management is on maintaining health by preventing nutritional and respiratory complications. The CF Foundation convened a committee to develop recommendations based on a systematic review of the evidence and expert opinion. These guidelines encompass monitoring and treatment recommendations for infants diagnosed with CF and are intended to help guide families, primary care providers, and specialty care centers in the care of infants with CF. (J Pediatr 2009; 155:S73-93).

引用

页码：S73 / S93

页数：21

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