Living related liver transplantation in 13 cases of progressive familial intrahepatic cholestasis

被引：29

作者：

Bassas, A

Chehab, M

Hebby, H

Al Shahed, M

Al Husseini, H

Al Zahrani, A

Wali, S

机构：

[1] Riyadh Armed Forces Hosp, Dept Surg, Riyadh 11159, Saudi Arabia

[2] Riyadh Armed Forces Hosp, Dept Pediat, Riyadh 11159, Saudi Arabia

[3] Riyadh Armed Forces Hosp, Dept Pediat, Riyadh 11159, Saudi Arabia

[4] Riyadh Armed Forces Hosp, Dept Radiol, Riyadh 11159, Saudi Arabia

[5] Riyadh Armed Forces Hosp, Dept Pathol, Riyadh 11159, Saudi Arabia

来源：

TRANSPLANTATION PROCEEDINGS | 2003年 / 35卷 / 08期

关键词：

D O I：

10.1016/j.transproceed.2003.10.047

中图分类号：

R392 [医学免疫学]; Q939.91 [免疫学];

学科分类号：

100102 ;

摘要：

Progressive familial intrahepatic cholestasis (PFIC) is a heterogenous group of disorders with various etiologies. Recent molecular and genetic studies have categorized the spectrum of types. Liver transplantation is a curative modality of treatment in this disease. We report our experience with 13 patients with PFIC who underwent living related liver transplantation. The follow-up periods ranged from 12 to 50 months. Two children died at 1 and 2 years posttransplantation, leading to a decrease in survival rate from 100% in the first year to 84.6%.

引用

页码：3003 / 3005

页数：3

共 21 条

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