Successful plasma therapy in hemolytic uremic syndrome with factor H deficiency

被引：35

作者：

Nathanson, S

Frémeaux-Bacchi, V

Deschênes, G

机构：

[1] Hop Armand Trousseau, Serv Nephrol Pediat, F-75571 Paris 12, France

[2] Hop Europeen Georges Pompidou, Serv Immunol Biol, F-75015 Paris, France

来源：

PEDIATRIC NEPHROLOGY | 2001年 / 16卷 / 07期

关键词：

hemolytic uremic syndrome; factor H; fresh frozen plasma; renal function;

D O I：

10.1007/s004670100609

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

A patient with homozygous factor H deficiency presented with hemolytic uremic syndrome (HUS) at the age of 7 months. After a 2-year period of stability, renal failure and erythrocyte fragmentation recurred between the age of 3 and 4 years. Fresh frozen plasma infusions allowed renal function to be improved and erythrocyte fragmentation to be stopped. Withdrawal of plasma therapy led to a relapse of the biological signs of HUS.

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收藏

页码：554 / 556

页数：3

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