Protein-losing enteropathy after fontan operation: Resolution after baffle fenestration

被引:26
作者
Jacobs, ML [1 ]
Rychik, J [1 ]
Byrum, CJ [1 ]
Norwood, WI [1 ]
机构
[1] CHILDRENS HOSP PHILADELPHIA,DIV CARDIOL,PHILADELPHIA,PA 19104
关键词
D O I
10.1016/0003-4975(95)00659-1
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
A 4-year-old child with hypoplastic left heart syndrome and a 6-year-old child with tricuspid atresia had both undergone staged reconstructive operations culminating in a Fontan operation. Peripheral edema, ascites, and hypoalbuminemia refractory to dietary manipulation and steroid therapy developed in both patients. After hemodynamic assessment, each child underwent surgical creation of a 4.8-mm fenestration in the previously placed baffle that separated the systemic venous pathway from the pulmonary venous atrium. Peripheral edema and ascites promptly resolved and serum protein levels normalized within 2 weeks after operation. Systemic arterial saturation is 86% in each child, and both children remain clinically well with no evidence of protein-losing enteropathy on normal diets and without specific medical therapy.
引用
收藏
页码:206 / 208
页数:3
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