Acquired idiopathic generalized anhidrosis with isolated sudomotor neuropathy

被引:15
作者
Miyazoe, S
Matsuo, H
Ohnishi, A
Tajima, F
Fujishita, S
Ichinose, K
Shibuya, N
机构
[1] Kawatana Natl Hosp, Dept Neurol, Kawatana 8593615, Nagasaki, Japan
[2] Univ Occupat & Environm Hlth, Dept Neurol, Kitakyushu, Fukuoka 807, Japan
[3] Univ Occupat & Environm Hlth, Dept Rehabil Med, Kitakyushu, Fukuoka 807, Japan
关键词
D O I
10.1002/ana.410440314
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
The pathogenesis and underlying lesion of acquired idiopathic generalized anhidrosis (AIGA) are apparently heterogeneous. We report a patient with AIGA in whom the eccrine glands were histologically normal. However, electron microscopic examination showed markedly low numbers of nerve terminals and unmyelinated axons associated with the eccrine glands. Our laboratory investigations suggest that degeneration of postganglionic sympathetic cholinergic nerve may be the underlying pathogenetic mechanism of anhidrosis in this patient.
引用
收藏
页码:378 / 381
页数:4
相关论文
共 14 条
[1]  
Aihara M, 1984, JPN J CLIN DERMATOL, V38, P619
[2]   ACQUIRED IDIOPATHIC GENERALIZED ANHIDROSIS - CLINICAL MANIFESTATIONS AND HISTOCHEMICAL-STUDIES [J].
ANDO, Y ;
FUJII, S ;
SAKASHITA, N ;
UCHINO, M ;
ANDO, M .
JOURNAL OF THE NEUROLOGICAL SCIENCES, 1995, 132 (01) :80-83
[3]   GENERAL ACQUIRED ANHYDROSIS [J].
ENGELHARDT, HT ;
MELVIN, JP .
AMERICAN JOURNAL OF THE MEDICAL SCIENCES, 1945, 210 (03) :323-328
[5]   PRURITUS AND ACQUIRED ANHIDROSIS - 2 UNUSUAL CASES [J].
KAY, DM ;
MAIBACH, HI .
ARCHIVES OF DERMATOLOGY, 1969, 100 (03) :291-&
[6]   QUANTITATIVE SUDOMOTOR AXON REFLEX TEST IN NORMAL AND NEUROPATHIC SUBJECTS [J].
LOW, PA ;
CASKEY, PE ;
TUCK, RR ;
FEALEY, RD ;
DYCK, PJ .
ANNALS OF NEUROLOGY, 1983, 14 (05) :573-580
[7]   CHRONIC IDIOPATHIC ANHIDROSIS [J].
LOW, PA ;
FEALEY, RD ;
SHEPS, SG ;
SU, WPD ;
TRAUTMANN, JC ;
KUNTZ, NL .
ANNALS OF NEUROLOGY, 1985, 18 (03) :344-348
[8]   ACQUIRED IDIOPATHIC GENERALIZED ANHIDROSIS - A DISTINCTIVE CLINICAL SYNDROME [J].
MURAKAMI, K ;
SOBUE, G ;
TERAO, S ;
MITSUMA, T .
JOURNAL OF NEUROLOGY, 1988, 235 (07) :428-431
[9]   SKIN SYMPATHETIC-NERVE ACTIVITY IN ACQUIRED IDIOPATHIC GENERALIZED ANHIDROSIS [J].
MURAKAMI, K ;
SOBUE, G ;
IWASE, S ;
MITSUMA, T ;
MANO, T .
NEUROLOGY, 1993, 43 (06) :1137-1140
[10]  
MUTA Y, 1991, CLIN NEUROL, V31, P1165