Successful medical treatment of severely decompensated Wilson disease

被引：5

作者：

Silva, EES

Sarles, J

Buts, JP

Sokal, EM

机构：

[1] UNIV CATHOLIQUE LOUVAIN, CLIN ST LUC, DEPT PEDIAT, BRUSSELS, BELGIUM

[2] HOSP UNIV LA TIMONE, HOP CTR, MARSEILLE, FRANCE

来源：

JOURNAL OF PEDIATRICS | 1996年 / 128卷 / 02期

关键词：

D O I：

暂无

中图分类号：

R72 [儿科学];

学科分类号：

100202 [儿科学];

摘要：

Delayed response to medical treatment sometimes leads to unnecessary liver transplantation in patients with severely decompensated Wilson disease. We report the course of five patients (mean age 13.4 years, range 11 to 15 years) with severely decompensated Wilson disease who were successfully treated medically. Prothrombin time improved after a minimum of 1 month and returned to normal within 3 months to 1 year or more.

引用

收藏

页码：285 / 287

页数：3

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