Management of patients with the hereditary long QT syndrome

被引：20

作者：

Moss, AJ ^{[1
]}

机构：

[1] Univ Rochester, Sch Med & Dent, Dept Med, Cardiol Unit, Rochester, NY USA

来源：

JOURNAL OF CARDIOVASCULAR ELECTROPHYSIOLOGY | 1998年 / 9卷 / 06期

关键词：

arrhythmias; torsades de pointes; syncope; sudden death; beta blockers; pacemakers; implantable cardioverter defibrillator;

D O I：

10.1111/j.1540-8167.1998.tb00952.x

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Long QT Syndrome. The hereditary long QT syndrome is an inherited ion channel disorder with QT prolongation, morphologic changes in the T waves, and a relatively high frequency of syncope, T wave alternans, torsades de pointes-type ventricular tachycardia, and sudden death. Monotherapy with beta blockers is the treatment of first choice. In patients with recurrent syncope despite therapy with beta blockers, pacemakers and/or ganglionectomy may be useful in selected cases with an implantable cardioverter defibrillator used as a fail-safe approach in high-risk patients.

引用

页码：668 / 674

页数：7

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