Hereditary angioedema

被引:179
作者
Cicardi, M
Agostoni, A
机构
关键词
D O I
10.1056/NEJM199606203342510
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:1666 / 1667
页数:2
相关论文
共 14 条
[1]   HEREDITARY AND ACQUIRED C1-INHIBITOR DEFICIENCY - BIOLOGICAL AND CLINICAL CHARACTERISTICS IN 235 PATIENTS [J].
AGOSTONI, A ;
CICARDI, M .
MEDICINE, 1992, 71 (04) :206-215
[2]   REDUCTION IN TRANSMISSION OF HEPATITIS-C AFTER THE INTRODUCTION OF A HEAT-TREATMENT STEP IN THE PRODUCTION OF C1-INHIBITOR CONCENTRATE [J].
CICARDI, M ;
MANNUCCI, PM ;
CASTELLI, R ;
RUMI, MG ;
AGOSTONI, A .
TRANSFUSION, 1995, 35 (03) :209-212
[3]  
CLEOPHAS TJM, 1995, J MOL MED, V73, P421
[4]   C1 INHIBITOR HINGE REGION MUTATIONS PRODUCE DYSFUNCTION BY DIFFERENT MECHANISMS [J].
DAVIS, AE ;
AULAK, K ;
PARAD, RB ;
STECKLEIN, HP ;
ELDERING, E ;
HACK, CE ;
KRAMER, J ;
STRUNK, RC ;
BISSLER, J ;
ROSEN, FS .
NATURE GENETICS, 1992, 1 (05) :354-358
[5]   A BIOCHEMICAL ABNORMALITY IN HEREDITARY ANGIONEUROTIC EDEMA - ABSENCE OF SERUM INHIBITOR OF C 1-ESTERASE [J].
DONALDSON, VH ;
EVANS, RR .
AMERICAN JOURNAL OF MEDICINE, 1963, 35 (01) :37-+
[6]   NONSENSE MUTATIONS AFFECT C1-INHIBITOR MESSENGER-RNA LEVELS IN PATIENTS WITH TYPE-I HEREDITARY ANGIONEUROTIC-EDEMA [J].
FRANGI, D ;
CICARDI, M ;
SICA, A ;
COLOTTA, F ;
AGOSTONI, A ;
DAVIS, AE .
JOURNAL OF CLINICAL INVESTIGATION, 1991, 88 (03) :755-759
[7]   Hepatitis C and pasteurized C1-inhibitor concentrate [J].
Klarmann, D ;
Kreuz, W ;
JosephSteiner, J ;
Ehrenforth, S .
TRANSFUSION, 1996, 36 (01) :84-85
[8]  
Milton J L, 1876, Edinb Med J, V22, P513
[9]   THE CONTINUING UNETHICAL USE OF PLACEBO CONTROLS [J].
ROTHMAN, KJ ;
MICHELS, KB .
NEW ENGLAND JOURNAL OF MEDICINE, 1994, 331 (06) :394-398
[10]   PREKALLIKREIN ACTIVATION AND HIGH-MOLECULAR-WEIGHT KININOGEN CONSUMPTION IN HEREDITARY ANGIOEDEMA [J].
SCHAPIRA, M ;
SILVER, LD ;
SCOTT, CF ;
SCHMAIER, AH ;
PROGRAIS, LJ ;
CURD, JG ;
COLMAN, RW .
NEW ENGLAND JOURNAL OF MEDICINE, 1983, 308 (18) :1050-1053