Linear IgA bullous dermatosis in a patient with chronic renal failure: Response to intravenous immunoglobulin therapy

被引:43
作者
Khan, IU
Bhol, KC
Ahmed, AR
机构
[1] Harvard Univ, Sch Med, Ctr Blood Res, New England Baptist Hosp,Dept Med, Boston, MA USA
[2] Harvard Univ, Sch Dent Med, Dept Oral Med, Boston, MA 02115 USA
关键词
D O I
10.1016/S0190-9622(99)70504-9
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
Linear IgA bullous dermatosis is a blistering disease with a heterogeneous clinical manifestation, characterized by deposition of IgA along the basement membrane zone of perilesional skin on direct immunofluorescence. We describe a patient with chronic renal failure who experienced linear IgA bullous dermatosis. Long-term administration of intravenous immunoglobulin therapy was associated with clinical remission lasting more than 12 months.
引用
收藏
页码:485 / 488
页数:4
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