Lethal cardiomyopathy in epidermolysis bullosa associated with amitriptyline

被引:12
作者
Taibjee, SM
Ramani, P
Brown, R
Moss, C
机构
[1] Birmingham Childrens Hosp, Dept Dermatol, Birmingham B4 6NH, W Midlands, England
[2] Birmingham Childrens Hosp, Dept Histopathol, Birmingham, W Midlands, England
关键词
D O I
10.1136/adc.2004.068775
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
There are previous reports of dilated cardiomyopathy (DCM) in recessive dystrophic epidermolysis bullosa (RDEB), a debilitating blistering skin disorder. The pathogenesis of DCM in RDEB remains uncertain, although dietary deficiency of selenium and carnitine have been implicated. A 6 year old girl with RDEB who died of DCM is reported; attention is drawn to the possible role of two potentially cardiotoxic drugs, amitriptyline and cisapride.
引用
收藏
页码:871 / 872
页数:2
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