Maladaptive behaviour in Prader-Willi syndrome in adult life

被引:41
作者
Clarke, DJ
Boer, H
Chung, MC
Sturmey, P
Webb, T
机构
[1] SAN ANTONIO STATE SCH,SAN ANTONIO,TX
[2] BIRMINGHAM MATERN HOSP,SUBDEPT GENET,BIRMINGHAM,W MIDLANDS,ENGLAND
关键词
Aberrant Behavior Checklist; maladaptive behaviour; mental retardation; Prader-Willi syndrome;
D O I
10.1111/j.1365-2788.1996.tb00617.x
中图分类号
G76 [特殊教育];
学科分类号
040109 ;
摘要
Thirty adults with Prader-Willi syndrome (PWS) were compared with 30 adults with non-specific learning disability matched for age, sex and severity of mental retardation. Maladaptive behaviour was assessed with the Aberrant Behavior Checklist (ABC), a 58-item structured interview which rates behaviours from 0 (not a problem) to 3 (severe problem) and which yields five factors (I) irritability, agitation; (II) lethargy, withdrawal; (III) stereotypic behavior; (IV) hyperactivity, noncompliance; and (V) inappropriate speech). The PWS sample had significantly higher factor I (P<0.001) and factor V (P<0.05) scores. The PWS sample had mean scores above 1 for 17 ABC items; the contrast subjects had no mean scores above 1. The factor I scores for the PWS sample were similar to those of inpatients in hospital facilities for adults with mental retardation and mental illness or severely challenging behaviour. The results support previous work, and extend it by suggesting that temper tantrums, self-injury, impulsiveness, lability of mood, inactivity and repetitive speech are characteristic behaviours in PWS in adult life. Studies of the reasons for heterogeneity in behaviour are now needed.
引用
收藏
页码:159 / 165
页数:7
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