Partial splenic embolization for treatment of disseminated intravascular coagulation in lymphangiomatosis

被引:12
作者
Patton, DF [1 ]
Kaye, R
Dickman, P
Blatt, J
机构
[1] Childrens Hosp Pittsburgh, Dept Pediat, Div Hematol Oncol, Pittsburgh, PA 15213 USA
[2] Childrens Hosp Pittsburgh, Dept Radiol, Div Hematol Oncol, Pittsburgh, PA 15213 USA
[3] Childrens Hosp Pittsburgh, Dept Pathol, Div Hematol Oncol, Pittsburgh, PA 15213 USA
关键词
D O I
10.1016/S0022-3476(98)70412-3
中图分类号
R72 [儿科学];
学科分类号
100202 [儿科学];
摘要
A 1-year-old boy presented with pericardial effusion, pulmonary infiltrates, and disseminated intravascular coagulation; lung biopsy indicated pulmonary lymphangiomatosis. He did not respond to medical therapy and was a poor surgical candidate; therefore, he underwent partial splenic embolization. The procedure resulted in a complete disappearance of the DIC and marked improvement in his cardiorespiratory status. He continues to thrive and is transfusion-independent 2 years after the procedure.
引用
收藏
页码:1057 / 1060
页数:4
相关论文
共 17 条
[1]
BIKFALVI A, 1994, LEUKEMIA, V8, P523
[2]
SPLENIC EMBOLIZATION IN CHILDREN - LONG-TERM EFFICACY [J].
BRANDT, CT ;
ROTHBARTH, LJ ;
KUMPE, D ;
KARRER, FM ;
LILLY, JR .
JOURNAL OF PEDIATRIC SURGERY, 1989, 24 (07) :642-645
[3]
LYMPHANGIOMYOMATOSIS - A REPORT OF 3 CASES TREATED WITH TAMOXIFEN [J].
CLEMM, C ;
JEHN, U ;
WOLFHORNUNG, B ;
SIEMON, G ;
WALTER, G .
KLINISCHE WOCHENSCHRIFT, 1987, 65 (08) :391-393
[4]
DICKERMAN JD, 1979, PEDIATRICS, V63, P938
[5]
DIETZ WH, 1977, J PEDIATR-US, V90, P421, DOI 10.1016/S0022-3476(77)80706-3
[6]
INTERFERON ALFA-2A THERAPY FOR LIFE-THREATENING HEMANGIOMAS OF INFANCY [J].
EZEKOWITZ, RAB ;
MULLIKEN, JB ;
FOLKMAN, J .
NEW ENGLAND JOURNAL OF MEDICINE, 1992, 326 (22) :1456-1463
[7]
CONGENITAL PULMONARY LYMPHANGIECTASIA [J].
HUBER, A ;
SCHRANZ, D ;
BLAHA, I ;
SCHMITTMECHELKE, T ;
SCHUMACHER, R .
PEDIATRIC PULMONOLOGY, 1991, 10 (04) :310-313
[8]
KESLO JM, 1991, CHEST, V100, P556
[9]
LYMPHANGIOMA OF THE LUNG ASSOCIATED WITH RESPIRATORY-DISTRESS IN A NEONATE [J].
MILOVIC, I ;
OLUIC, D .
PEDIATRIC RADIOLOGY, 1992, 22 (02) :156-156
[10]
PARTIAL SPLENIC EMBOLIZATION FOR THE TREATMENT OF CHRONIC IDIOPATHIC THROMBOCYTOPENIC PURPURA [J].
MIYAZAKI, M ;
ITOH, H ;
KAIHO, T ;
OHTAWA, S ;
AMBIRU, S ;
HAYASHI, S ;
NAKAJIMA, N ;
OH, H ;
ASAI, T ;
ISEKI, T .
AMERICAN JOURNAL OF ROENTGENOLOGY, 1994, 163 (01) :123-126