Resolution of xanthomas in Alagille syndrome after liver transplantation

被引：16

作者：

Buckley, DA ^{[1
]}

Higgins, EM ^{[1
]}

du Vivier, AWP ^{[1
]}

机构：

[1] Univ London Kings Coll Hosp, Dept Dermatol, London SE5 9RS, England

来源：

PEDIATRIC DERMATOLOGY | 1998年 / 15卷 / 03期

关键词：

D O I：

10.1046/j.1525-1470.1998.1998015199.x

中图分类号：

R75 [皮肤病学与性病学];

学科分类号：

100206 ;

摘要：

Alagille syndrome (arteriohepatic dysplasia) is a genetic disorder with autosomal dominant transmission which has been localized to chromosome 20p, Cutaneous manifestations include jaundice, pruritus, and widespread xanthomata, We report a child with severe Alagille syndrome in whom orthotopic liver transplantation caused rapid resolution of disfiguring xanthomas.

引用

页码：199 / 202

页数：4

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