Serum KL-6 level as a monitoring marker in a patient with pulmonary alveolar proteinosis

被引:23
作者
Nakajima, M
Manabe, T
Niki, Y
Matsushima, T
机构
[1] Kawasaki Med Sch, Div Resp Dis, Dept Internal Med, Kurashiki, Okayama 7010192, Japan
[2] Kawasaki Med Sch, Dept Pathol, Kurashiki, Okayama 7010192, Japan
关键词
KL-6; pulmonary alveolar proteinosis; tumour marker;
D O I
10.1136/thx.53.9.809
中图分类号
R56 [呼吸系及胸部疾病];
学科分类号
摘要
A raised serum level of KL-6 is known to exist in active pulmonary fibrosis and KL-6 may be produced and secreted by type II pneumocytes. A case is described of pulmonary alveolar proteinosis with high serum KL-6 levels. The serum KL-6 level decreased after whole lung washing and correlated with symptoms, opacities on the chest radiograph, and arterial blood gas measurements. The serum KL-6 level may represent a useful marker for pulmonary alveolar proteinosis.
引用
收藏
页码:809 / 811
页数:3
相关论文
共 11 条
[1]   ALVEOLAR PHOSPHOLIPIDS IN PULMONARY ALVEOLAR PROTEINOSIS [J].
AKINO, T ;
OKANO, G ;
OHNO, K .
TOHOKU JOURNAL OF EXPERIMENTAL MEDICINE, 1978, 126 (01) :51-62
[2]   PULMONARY INTERSTITIAL FIBROSIS ASSOCIATED WITH ALVEOLAR PROTEINOSIS [J].
CLAGUE, HW ;
WALLACE, AC ;
MORGAN, WKC .
THORAX, 1983, 38 (11) :865-866
[3]   UPDATE ON THE CLINICAL-DIAGNOSIS, MANAGEMENT, AND PATHOGENESIS OF PULMONARY ALVEOLAR PROTEINOSIS (PHOSPHOLIPIDOSIS) [J].
CLAYPOOL, WD ;
ROGERS, RM ;
MATUSCHAK, GM .
CHEST, 1984, 85 (04) :550-558
[4]  
GILMORE LB, 1988, AM J PATHOL, V133, P252
[5]   MONITORING OF SERUM KL-6 ANTIGEN IN A PATIENT WITH RADIATION PNEUMONIA [J].
HAMADA, H ;
KOHNO, N ;
AKIYAMA, M ;
HIWADA, K .
CHEST, 1992, 101 (03) :858-860
[6]   NEW SERUM INDICATOR OF INTERSTITIAL PNEUMONITIS ACTIVITY - SIALYLATED CARBOHYDRATE ANTIGEN KL-6 [J].
KOHNO, N ;
KYOIZUMI, S ;
AWAYA, Y ;
FUKUHARA, H ;
YAMAKIDO, M ;
AKIYAMA, M .
CHEST, 1989, 96 (01) :68-73
[7]   KL-6, A MUCIN-LIKE GLYCOPROTEIN, IN BRONCHOALVEOLAR LAVAGE FLUID FROM PATIENTS WITH INTERSTITIAL LUNG-DISEASE [J].
KOHNO, N ;
AWAYA, Y ;
OYAMA, T ;
YAMAKIDO, M ;
AKIYAMA, M ;
INOUE, Y ;
YOKOYAMA, A ;
HAMADA, H ;
FUJIOKA, S ;
HIWADA, K .
AMERICAN REVIEW OF RESPIRATORY DISEASE, 1993, 148 (03) :637-642
[8]  
KOHNO N, 1994, INT J CANCER, P81
[9]  
NAKAJIMA M, 1994, JPN J THORAC DIS, V32, P1109
[10]  
NAKAJIMA M, 1995, AM J RESP CRIT CARE, V151, pA541