Absent meibomian glands: A marker for EEC syndrome

被引:20
作者
Bonnar, E
Logan, P
Eustace, P
机构
[1] University Department of Ophthalmology, Mater Misericordiae Hospital, Dublin, Eccles Street
关键词
EEC syndrome; ectodermal dysplasia; meibomian glands; blepharitis; keratitis; penetrating keratoplasty;
D O I
10.1038/eye.1996.73
中图分类号
R77 [眼科学];
学科分类号
100212 ;
摘要
A patient with a 20 year history of severe keratoconjunctivitis of unknown origin was found, on assessment at a blepharitis clinic, to have complete absence of meibomian glands. Further examination revealed the features of EEC syndrome. To our knowledge, this is the only case to have been diagnosed in this way. The ocular complications of EEC syndrome and other ectodermal dysplasias are reviewed.
引用
收藏
页码:355 / 361
页数:7
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