Hypoplastic left heart syndrome with restrictive atrial septal defect and congenital pulmonary lymphangiectasis

被引:14
作者
Luciani, GB
Pessotto, R
Mombello, A
Mazzucco, A
机构
[1] Univ Verona, Div Cardiac Surg, I-37126 Verona, Italy
[2] Univ Verona, Div Pathol, I-37126 Verona, Italy
关键词
D O I
10.1016/S1054-8807(98)00012-X
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
The presence of a restrictive atrial septal defect in hypoplastic left heart syndrome represents a surgical emergency and may negatively affect survival after operation. A neonate with such a disease association, requiring septectomy upon birth developed intractable respiratory failure due to congenital pulmonary lymphangiectasis. The therapeutic implications of this rare pathologic condition an discussed. (C) 1998 by Elsevier Science Inc.
引用
收藏
页码:49 / 51
页数:3
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