Manifestations of scleroderma pulmonary disease

被引:52
作者
Minai, OA [1 ]
Dweik, RA [1 ]
Arroliga, AC [1 ]
机构
[1] Cleveland Clin Fdn, Dept Pulm & Crit Care Med, Cleveland, OH 44195 USA
关键词
D O I
10.1016/S0272-5231(05)70112-X
中图分类号
R56 [呼吸系及胸部疾病];
学科分类号
摘要
Scleroderma is a multisystem disease of unknown cause characterized by synthesis and deposition of excessive extracellular matrix and vascular obliteration. Pulmonary involvement is a significant cause of morbidity and mortality. This article gives an overview of the pulmonary manifestations of scleroderma and discusses diagnostic and therapeutic options.
引用
收藏
页码:713 / +
页数:21
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